Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report

Chiari type 1 malformations are characterised by caudal descent of cerebellar tonsil into foramen magnum. Usually it is congenital. Paget’s disease causing acquired chiari type 1 malformation is rare with only five reported cases in the literature. The diagnosis is primarily by Magnetic Resonance...

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Autores principales:	Srestha Khan, Senthil Kumar Aiyappan, Abinesh Govindarajan, Vinayagam Shanmugam
Formato:	article
Lenguaje:	EN
Publicado:	JCDR Research and Publications Private Limited 2021
Materias:	cerebellar tonsil herniation computed tomography magnetic resonance imaging Medicine R
Acceso en línea:	https://doaj.org/article/020ee8a5b4e64c218b632fd633f1a952
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spelling	oai:doaj.org-article:020ee8a5b4e64c218b632fd633f1a9522021-11-12T14:13:55ZAcquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report10.7860/JCDR/2021/50656.153732249-782X0973-709Xhttps://doaj.org/article/020ee8a5b4e64c218b632fd633f1a9522021-09-01T00:00:00Zhttps://www.jcdr.net/articles/PDF/15373/50656_CE[Ra1]_F[SH]_PF1(SC_SHU)_PFA(SC_KM)_PN(KM).pdfhttps://doaj.org/toc/2249-782Xhttps://doaj.org/toc/0973-709XChiari type 1 malformations are characterised by caudal descent of cerebellar tonsil into foramen magnum. Usually it is congenital. Paget’s disease causing acquired chiari type 1 malformation is rare with only five reported cases in the literature. The diagnosis is primarily by Magnetic Resonance Imaging (MRI). Authors reported a case of acquired chiari type 1 malformation due to paget’s disease in a 58-year-old male patient diagnosed by MRI and Computed Tomography (CT). The patient presented with complaints of headache, unsteady gait, slow movements with weakness in all the four limbs, difficulty in walking which aggravated since three days and stammering of speech. Initially a diagnosis of motor neuron disease was suspected and the patient was subjected for MRI examination of brain and spine. MRI revealed platybasia with cerebellar tonsillar herniation with calvarial thickening and multiple vertebral collapse. The CT of brain and spine was done to evaluate bones specifically in view of thickened cranial vault and multiple vertebral collapse on MRI which revealed features of paget’s disease in the form of widened sclerotic bone with lytic areas and thickened trabeculae. Hence, diagnosis of paget’s disease causing acquired chiari type 1 malformation was made which correlated with biochemical findings. The management is different in primary and acquired chiari type 1 malformation and hence it is important to diagnose this condition which is relatively rare.Srestha KhanSenthil Kumar AiyappanAbinesh GovindarajanVinayagam ShanmugamJCDR Research and Publications Private Limitedarticlecerebellar tonsil herniationcomputed tomographymagnetic resonance imagingMedicineRENJournal of Clinical and Diagnostic Research, Vol 15, Iss 9, Pp TD01-TD02 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	cerebellar tonsil herniation computed tomography magnetic resonance imaging Medicine R
spellingShingle	cerebellar tonsil herniation computed tomography magnetic resonance imaging Medicine R Srestha Khan Senthil Kumar Aiyappan Abinesh Govindarajan Vinayagam Shanmugam Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report
description	Chiari type 1 malformations are characterised by caudal descent of cerebellar tonsil into foramen magnum. Usually it is congenital. Paget’s disease causing acquired chiari type 1 malformation is rare with only five reported cases in the literature. The diagnosis is primarily by Magnetic Resonance Imaging (MRI). Authors reported a case of acquired chiari type 1 malformation due to paget’s disease in a 58-year-old male patient diagnosed by MRI and Computed Tomography (CT). The patient presented with complaints of headache, unsteady gait, slow movements with weakness in all the four limbs, difficulty in walking which aggravated since three days and stammering of speech. Initially a diagnosis of motor neuron disease was suspected and the patient was subjected for MRI examination of brain and spine. MRI revealed platybasia with cerebellar tonsillar herniation with calvarial thickening and multiple vertebral collapse. The CT of brain and spine was done to evaluate bones specifically in view of thickened cranial vault and multiple vertebral collapse on MRI which revealed features of paget’s disease in the form of widened sclerotic bone with lytic areas and thickened trabeculae. Hence, diagnosis of paget’s disease causing acquired chiari type 1 malformation was made which correlated with biochemical findings. The management is different in primary and acquired chiari type 1 malformation and hence it is important to diagnose this condition which is relatively rare.
format	article
author	Srestha Khan Senthil Kumar Aiyappan Abinesh Govindarajan Vinayagam Shanmugam
author_facet	Srestha Khan Senthil Kumar Aiyappan Abinesh Govindarajan Vinayagam Shanmugam
author_sort	Srestha Khan
title	Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report
title_short	Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report
title_full	Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report
title_fullStr	Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report
title_full_unstemmed	Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report
title_sort	acquired chiari type 1 malformation secondary to paget’s disease of the bone: a case report
publisher	JCDR Research and Publications Private Limited
publishDate	2021
url	https://doaj.org/article/020ee8a5b4e64c218b632fd633f1a952
work_keys_str_mv	AT sresthakhan acquiredchiaritype1malformationsecondarytopagetsdiseaseoftheboneacasereport AT senthilkumaraiyappan acquiredchiaritype1malformationsecondarytopagetsdiseaseoftheboneacasereport AT abineshgovindarajan acquiredchiaritype1malformationsecondarytopagetsdiseaseoftheboneacasereport AT vinayagamshanmugam acquiredchiaritype1malformationsecondarytopagetsdiseaseoftheboneacasereport
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Acquired Chiari Type 1 Malformation Secondary to Paget’s Disease of the Bone: A Case Report

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