Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris

Congenital extrahepatic portosystemic shunts (ECPSS) are rare developmental anomalies in which a variable portion of the portal blood bypasses the liver and is shunted in the systemic circulation via one or more aberrant vessels. We present a clinical case of a 70-year-old man, who was referred to t...

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Autores principales:	Gandileva V., Makaveeva P., Tabakova D., Valerieva T., Simova I., Petkov P., Niagolova S., Hristov V., Poposki S., Dimitrov N., Vekov T.
Formato:	article
Lenguaje:	EN
Publicado:	Sciendo 2021
Materias:	abernethy malformation portal vein shunt congenital Medicine R
Acceso en línea:	https://doaj.org/article/06d3142d94a34036ade982e364d04133
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spelling	oai:doaj.org-article:06d3142d94a34036ade982e364d041332021-12-05T14:11:05ZAbernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris2719-538410.2478/amb-2021-0044https://doaj.org/article/06d3142d94a34036ade982e364d041332021-11-01T00:00:00Zhttps://doi.org/10.2478/amb-2021-0044https://doaj.org/toc/2719-5384Congenital extrahepatic portosystemic shunts (ECPSS) are rare developmental anomalies in which a variable portion of the portal blood bypasses the liver and is shunted in the systemic circulation via one or more aberrant vessels. We present a clinical case of a 70-year-old man, who was referred to the Cardiology Department because of exertional dyspnea, fatigue, and feeling of heaviness and pressure behind the sternum. MDCT of the aorta was performed and an aberrant vessel was discovered with communication with the left iliac vein on one side and superior mesenteric and splenic veins on the other. The portal vein was hypoplastic. The radiologic findings were suggestive of malformation of Abernethy. The ECPSS can be classified into 2 main groups (with complete and partial shunting). The patients have different clinical presentation. Some of them are completely asymptomatic while in others the shunt can manifest even before birth as fetal growth retardation or in the early neonatal period with neonatal cholestasis and galactosemia. Common complications are hepatic encephalopathy and hepatopulmonary syndrome and there is a wide variety of concomitant abnormalities. The imaging modalities play a crucial role in the diagnosis, classification, follow-up and the proper choice of therapeutic management in patients with ECPSS.Gandileva V.Makaveeva P.Tabakova D.Valerieva T.Simova I.Petkov P.Niagolova S.Hristov V.Poposki S.Dimitrov N.Vekov T.Sciendoarticleabernethy malformationportal veinshuntcongenitalMedicineRENActa Medica Bulgarica, Vol 48, Iss 4, Pp 23-27 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	abernethy malformation portal vein shunt congenital Medicine R
spellingShingle	abernethy malformation portal vein shunt congenital Medicine R Gandileva V. Makaveeva P. Tabakova D. Valerieva T. Simova I. Petkov P. Niagolova S. Hristov V. Poposki S. Dimitrov N. Vekov T. Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris
description	Congenital extrahepatic portosystemic shunts (ECPSS) are rare developmental anomalies in which a variable portion of the portal blood bypasses the liver and is shunted in the systemic circulation via one or more aberrant vessels. We present a clinical case of a 70-year-old man, who was referred to the Cardiology Department because of exertional dyspnea, fatigue, and feeling of heaviness and pressure behind the sternum. MDCT of the aorta was performed and an aberrant vessel was discovered with communication with the left iliac vein on one side and superior mesenteric and splenic veins on the other. The portal vein was hypoplastic. The radiologic findings were suggestive of malformation of Abernethy. The ECPSS can be classified into 2 main groups (with complete and partial shunting). The patients have different clinical presentation. Some of them are completely asymptomatic while in others the shunt can manifest even before birth as fetal growth retardation or in the early neonatal period with neonatal cholestasis and galactosemia. Common complications are hepatic encephalopathy and hepatopulmonary syndrome and there is a wide variety of concomitant abnormalities. The imaging modalities play a crucial role in the diagnosis, classification, follow-up and the proper choice of therapeutic management in patients with ECPSS.
format	article
author	Gandileva V. Makaveeva P. Tabakova D. Valerieva T. Simova I. Petkov P. Niagolova S. Hristov V. Poposki S. Dimitrov N. Vekov T.
author_facet	Gandileva V. Makaveeva P. Tabakova D. Valerieva T. Simova I. Petkov P. Niagolova S. Hristov V. Poposki S. Dimitrov N. Vekov T.
author_sort	Gandileva V.
title	Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris
title_short	Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris
title_full	Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris
title_fullStr	Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris
title_full_unstemmed	Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris
title_sort	abernethy malformation type ii in a 70-year-old patient with angina pectoris
publisher	Sciendo
publishDate	2021
url	https://doaj.org/article/06d3142d94a34036ade982e364d04133
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Abernethy Malformation Type II in a 70-Year-Old Patient with Angina Pectoris

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