Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome

Background: Spinal hamartoma is an extremely rare lesion for symptomatic spinal cord compression in adult population. Without any association of spinal dysraphism and neurofibromatosis, only 3 cases have been reported in the literature. Case description: A 40-year-old man presented with lumbago femo...

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Autores principales: Nazmin Ahmed, Shahidul Khan, KM Tarikul Islam, Avijit Dey, Vishal Chavda, Ottavio Tomasi, Gianluca Scalia, Giuseppe E. Umana, Bipin Chaurasia
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Publicado: Al-Azhar University, Faculty of Medicine (Damietta) 2021
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Acceso en línea:https://doaj.org/article/25dd1a45dcb34951b26a7ce65e14309d
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spelling oai:doaj.org-article:25dd1a45dcb34951b26a7ce65e14309d2021-12-02T19:02:51ZAdult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome2636-41742682-378010.21608/ijma.2021.66305.1279https://doaj.org/article/25dd1a45dcb34951b26a7ce65e14309d2021-07-01T00:00:00Zhttps://ijma.journals.ekb.eg/article_160652_7a0bbe9d7c5cd1a6ecf9cc5edd7e61b0.pdfhttps://doaj.org/toc/2636-4174https://doaj.org/toc/2682-3780Background: Spinal hamartoma is an extremely rare lesion for symptomatic spinal cord compression in adult population. Without any association of spinal dysraphism and neurofibromatosis, only 3 cases have been reported in the literature. Case description: A 40-year-old man presented with lumbago femorica for 6 months. Gradually the symptoms worsened and he developed features of Cauda equina syndrome. Magnetic Resonence Imagimg demonstrated a heterogeneously hyperintense intradural extramedullary mass in both T1 and T2WI, involving conus medullaris and cauda equina, opposite to L1. Patient underwent near total resection of lesion through posterior midline approach. Histopathological features were consistent with hamartoma. Patient neurologically improved and follow up MRI at 6 months showed static small nodular tumor residue. Conclusion: To the best of our knowledge, current report is the fourth case of spinal hamartoma in adult male, without any association of spinal dysraphism and neurofibromatosis .This may be the first reported case from Bangladesh.Nazmin AhmedShahidul KhanKM Tarikul IslamAvijit DeyVishal ChavdaOttavio TomasiGianluca ScaliaGiuseppe E. UmanaBipin ChaurasiaAl-Azhar University, Faculty of Medicine (Damietta)articlehamartomaneurofibromatosisspinal dysraphismMedicine (General)R5-920ENInternational Journal of Medical Arts, Vol 3, Iss 3, Pp 1556-1561 (2021)
institution DOAJ
collection DOAJ
language EN
topic hamartoma
neurofibromatosis
spinal dysraphism
Medicine (General)
R5-920
spellingShingle hamartoma
neurofibromatosis
spinal dysraphism
Medicine (General)
R5-920
Nazmin Ahmed
Shahidul Khan
KM Tarikul Islam
Avijit Dey
Vishal Chavda
Ottavio Tomasi
Gianluca Scalia
Giuseppe E. Umana
Bipin Chaurasia
Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome
description Background: Spinal hamartoma is an extremely rare lesion for symptomatic spinal cord compression in adult population. Without any association of spinal dysraphism and neurofibromatosis, only 3 cases have been reported in the literature. Case description: A 40-year-old man presented with lumbago femorica for 6 months. Gradually the symptoms worsened and he developed features of Cauda equina syndrome. Magnetic Resonence Imagimg demonstrated a heterogeneously hyperintense intradural extramedullary mass in both T1 and T2WI, involving conus medullaris and cauda equina, opposite to L1. Patient underwent near total resection of lesion through posterior midline approach. Histopathological features were consistent with hamartoma. Patient neurologically improved and follow up MRI at 6 months showed static small nodular tumor residue. Conclusion: To the best of our knowledge, current report is the fourth case of spinal hamartoma in adult male, without any association of spinal dysraphism and neurofibromatosis .This may be the first reported case from Bangladesh.
format article
author Nazmin Ahmed
Shahidul Khan
KM Tarikul Islam
Avijit Dey
Vishal Chavda
Ottavio Tomasi
Gianluca Scalia
Giuseppe E. Umana
Bipin Chaurasia
author_facet Nazmin Ahmed
Shahidul Khan
KM Tarikul Islam
Avijit Dey
Vishal Chavda
Ottavio Tomasi
Gianluca Scalia
Giuseppe E. Umana
Bipin Chaurasia
author_sort Nazmin Ahmed
title Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome
title_short Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome
title_full Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome
title_fullStr Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome
title_full_unstemmed Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome
title_sort adult spinal hamartoma involving conus medullaris: brief review about associated congenital abnormalities and surgical outcome
publisher Al-Azhar University, Faculty of Medicine (Damietta)
publishDate 2021
url https://doaj.org/article/25dd1a45dcb34951b26a7ce65e14309d
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