Desmoid tumor initially unresectable – About two cases

Desmoid tumor, also called aggressive fibromatosis, is a rare fibroblastic proliferation of connective tissue and skeletal muscle aponeurosis. The aetiology of desmoid tumours is poorly understood, but they have been related with oestrogen stimuli, previous trauma, surgical interventions and pregnan...

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Autores principales:	Sara Senti Farraraons, Anna Estival Gonzalez, Cuadrado Velazquez, Clara Gene Skrabec, Ignasi Camps Ausas
Formato:	article
Lenguaje:	EN
Publicado:	Shiraz University of Medical Sciences 2019
Materias:	desmoid surgery oncology tumour Medicine R
Acceso en línea:	https://doaj.org/article/2b2223cbbde94231a04aeeab7034bcdc
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spelling	oai:doaj.org-article:2b2223cbbde94231a04aeeab7034bcdc2021-11-14T08:42:28ZDesmoid tumor initially unresectable – About two cases2783-243010.30476/acrr.2019.45966https://doaj.org/article/2b2223cbbde94231a04aeeab7034bcdc2019-12-01T00:00:00Zhttps://colorectalresearch.sums.ac.ir/article_45966_d0e1902a040e5d559a146f0ea0f0f93f.pdfhttps://doaj.org/toc/2783-2430Desmoid tumor, also called aggressive fibromatosis, is a rare fibroblastic proliferation of connective tissue and skeletal muscle aponeurosis. The aetiology of desmoid tumours is poorly understood, but they have been related with oestrogen stimuli, previous trauma, surgical interventions and pregnancy. Although it is characterized by not having potential for metastasize or differentiate, it is a non-encapsulated lesion, with an infiltrative growth and unpredictable behaviour. In this way, it could have either an aggressive pattern, when compared with other low degree malignancy sarcomas, or a very indolent one, even with spontaneous regression. Therapeutic options in desmoid tumours have been changing over these last years, as surgery upfront in asymptomatic patients has been superseded by active surveillance. However, treatment has to be individualized in some specific scenarios such as intra-abdominal lesions. We present two cases of patients diagnosed with an intra-abdominal desmoid tumour with threatening behaviour, the treatment approach and final resolution.Sara Senti FarraraonsAnna Estival GonzalezCuadrado VelazquezClara Gene SkrabecIgnasi Camps AusasShiraz University of Medical SciencesarticledesmoidsurgeryoncologytumourMedicineRENIranian Journal of Colorectal Research, Vol 7, Iss 4, Pp 1-4 (2019)
institution	DOAJ
collection	DOAJ
language	EN
topic	desmoid surgery oncology tumour Medicine R
spellingShingle	desmoid surgery oncology tumour Medicine R Sara Senti Farraraons Anna Estival Gonzalez Cuadrado Velazquez Clara Gene Skrabec Ignasi Camps Ausas Desmoid tumor initially unresectable – About two cases
description	Desmoid tumor, also called aggressive fibromatosis, is a rare fibroblastic proliferation of connective tissue and skeletal muscle aponeurosis. The aetiology of desmoid tumours is poorly understood, but they have been related with oestrogen stimuli, previous trauma, surgical interventions and pregnancy. Although it is characterized by not having potential for metastasize or differentiate, it is a non-encapsulated lesion, with an infiltrative growth and unpredictable behaviour. In this way, it could have either an aggressive pattern, when compared with other low degree malignancy sarcomas, or a very indolent one, even with spontaneous regression. Therapeutic options in desmoid tumours have been changing over these last years, as surgery upfront in asymptomatic patients has been superseded by active surveillance. However, treatment has to be individualized in some specific scenarios such as intra-abdominal lesions. We present two cases of patients diagnosed with an intra-abdominal desmoid tumour with threatening behaviour, the treatment approach and final resolution.
format	article
author	Sara Senti Farraraons Anna Estival Gonzalez Cuadrado Velazquez Clara Gene Skrabec Ignasi Camps Ausas
author_facet	Sara Senti Farraraons Anna Estival Gonzalez Cuadrado Velazquez Clara Gene Skrabec Ignasi Camps Ausas
author_sort	Sara Senti Farraraons
title	Desmoid tumor initially unresectable – About two cases
title_short	Desmoid tumor initially unresectable – About two cases
title_full	Desmoid tumor initially unresectable – About two cases
title_fullStr	Desmoid tumor initially unresectable – About two cases
title_full_unstemmed	Desmoid tumor initially unresectable – About two cases
title_sort	desmoid tumor initially unresectable – about two cases
publisher	Shiraz University of Medical Sciences
publishDate	2019
url	https://doaj.org/article/2b2223cbbde94231a04aeeab7034bcdc
work_keys_str_mv	AT sarasentifarraraons desmoidtumorinitiallyunresectableabouttwocases AT annaestivalgonzalez desmoidtumorinitiallyunresectableabouttwocases AT cuadradovelazquez desmoidtumorinitiallyunresectableabouttwocases AT clarageneskrabec desmoidtumorinitiallyunresectableabouttwocases AT ignasicampsausas desmoidtumorinitiallyunresectableabouttwocases
_version_	1718429767104987136

Desmoid tumor initially unresectable – About two cases

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