From 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment

Pulmonary arteriovenous malformations (PAVMs) are abnormal communications between the pulmonary artery and pulmonary vein without an intervening capillary system. PAVMs are most commonly associated with Hereditary Hemorrhagic Telangiectasia (HHT) also known as Osler-Weber-Rendu syndrome, a rare auto...

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Autores principales: Maciej Szmygin, Michał Sojka, Krzysztof Pyra, Tomasz Jargiełło
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Publicado: Termedia Publishing House 2020
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Acceso en línea:https://doaj.org/article/2c1d53b71e2e45a1bc1fb8ebf28cda07
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spelling oai:doaj.org-article:2c1d53b71e2e45a1bc1fb8ebf28cda072021-12-02T18:55:08ZFrom 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment1734-93381897-429510.5114/aic.2020.99277https://doaj.org/article/2c1d53b71e2e45a1bc1fb8ebf28cda072020-10-01T00:00:00Zhttps://www.termedia.pl/From-78-oxygen-saturation-to-95-in-60-minutes-r-nOsler-Weber-Rendu-syndrome-endovascular-treatment,35,41863,1,1.htmlhttps://doaj.org/toc/1734-9338https://doaj.org/toc/1897-4295Pulmonary arteriovenous malformations (PAVMs) are abnormal communications between the pulmonary artery and pulmonary vein without an intervening capillary system. PAVMs are most commonly associated with Hereditary Hemorrhagic Telangiectasia (HHT) also known as Osler-Weber-Rendu syndrome, a rare autosomal dominant disorder [1]. Acquired PAVMs occur in patients with chronic liver disease, history of cardiosurgical procedures or thoracic trauma, metastatic thyroid cancer or Fanconi syndrome [2]. The presenting symptoms including dyspnea, hypoxemia and chest pain result from right-to-left shunt, cardiac volume overload and destruction of lung parenchyma. Establishing the final diagnosis is difficult and requires multi-disciplinary workup. Traditional surgical management of PAVM has been gradually replaced by minimally invasive embolotherapy which became a gold standard of treatment [3].Maciej SzmyginMichał SojkaKrzysztof PyraTomasz JargiełłoTermedia Publishing HousearticleMedicineRENAdvances in Interventional Cardiology, Vol 16, Iss 3, Pp 354-355 (2020)
institution DOAJ
collection DOAJ
language EN
topic Medicine
R
spellingShingle Medicine
R
Maciej Szmygin
Michał Sojka
Krzysztof Pyra
Tomasz Jargiełło
From 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment
description Pulmonary arteriovenous malformations (PAVMs) are abnormal communications between the pulmonary artery and pulmonary vein without an intervening capillary system. PAVMs are most commonly associated with Hereditary Hemorrhagic Telangiectasia (HHT) also known as Osler-Weber-Rendu syndrome, a rare autosomal dominant disorder [1]. Acquired PAVMs occur in patients with chronic liver disease, history of cardiosurgical procedures or thoracic trauma, metastatic thyroid cancer or Fanconi syndrome [2]. The presenting symptoms including dyspnea, hypoxemia and chest pain result from right-to-left shunt, cardiac volume overload and destruction of lung parenchyma. Establishing the final diagnosis is difficult and requires multi-disciplinary workup. Traditional surgical management of PAVM has been gradually replaced by minimally invasive embolotherapy which became a gold standard of treatment [3].
format article
author Maciej Szmygin
Michał Sojka
Krzysztof Pyra
Tomasz Jargiełło
author_facet Maciej Szmygin
Michał Sojka
Krzysztof Pyra
Tomasz Jargiełło
author_sort Maciej Szmygin
title From 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment
title_short From 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment
title_full From 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment
title_fullStr From 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment
title_full_unstemmed From 78% oxygen saturation to 95% in 60 minutes: Osler-Weber-Rendu syndrome endovascular treatment
title_sort from 78% oxygen saturation to 95% in 60 minutes: osler-weber-rendu syndrome endovascular treatment
publisher Termedia Publishing House
publishDate 2020
url https://doaj.org/article/2c1d53b71e2e45a1bc1fb8ebf28cda07
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AT krzysztofpyra from78oxygensaturationto95in60minutesoslerweberrendusyndromeendovasculartreatment
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