Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)

Ebstein’s anomaly is characterized by the apical displacement of the septal and posterior leaflets of the tricuspid valve with atrialization of the right ventricle (RV). It is commonly associated with other heart defects including left ventricular noncompaction. We describe a case of prenatally diag...

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Autores principales:	Mohammad Mehdi, Snigdha Bhatia, Mehul Patel, Ashraf Aly
Formato:	article
Lenguaje:	EN
Publicado:	Hindawi Limited 2021
Materias:	Pediatrics RJ1-570
Acceso en línea:	https://doaj.org/article/2c5f683a9368440c89b7387a97a5090d
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spelling	oai:doaj.org-article:2c5f683a9368440c89b7387a97a5090d2021-11-22T01:09:58ZEbstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)2090-681110.1155/2021/9969588https://doaj.org/article/2c5f683a9368440c89b7387a97a5090d2021-01-01T00:00:00Zhttp://dx.doi.org/10.1155/2021/9969588https://doaj.org/toc/2090-6811Ebstein’s anomaly is characterized by the apical displacement of the septal and posterior leaflets of the tricuspid valve with atrialization of the right ventricle (RV). It is commonly associated with other heart defects including left ventricular noncompaction. We describe a case of prenatally diagnosed Ebstein’s anomaly in association with left ventricular noncompaction and a septal defect between the left ventricle and the atrialized portion of the RV (Gerbode-like defect). The patient underwent a modified Blalock−Taussig shunt followed by Glenn procedure because of severe RV hypoplasia and RV outflow tract obstruction. The patient tolerated both procedures and is doing clinically well in anticipation of Fontan procedure for single ventricle palliation.Mohammad MehdiSnigdha BhatiaMehul PatelAshraf AlyHindawi LimitedarticlePediatricsRJ1-570ENCase Reports in Pediatrics, Vol 2021 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	Pediatrics RJ1-570
spellingShingle	Pediatrics RJ1-570 Mohammad Mehdi Snigdha Bhatia Mehul Patel Ashraf Aly Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)
description	Ebstein’s anomaly is characterized by the apical displacement of the septal and posterior leaflets of the tricuspid valve with atrialization of the right ventricle (RV). It is commonly associated with other heart defects including left ventricular noncompaction. We describe a case of prenatally diagnosed Ebstein’s anomaly in association with left ventricular noncompaction and a septal defect between the left ventricle and the atrialized portion of the RV (Gerbode-like defect). The patient underwent a modified Blalock−Taussig shunt followed by Glenn procedure because of severe RV hypoplasia and RV outflow tract obstruction. The patient tolerated both procedures and is doing clinically well in anticipation of Fontan procedure for single ventricle palliation.
format	article
author	Mohammad Mehdi Snigdha Bhatia Mehul Patel Ashraf Aly
author_facet	Mohammad Mehdi Snigdha Bhatia Mehul Patel Ashraf Aly
author_sort	Mohammad Mehdi
title	Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)
title_short	Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)
title_full	Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)
title_fullStr	Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)
title_full_unstemmed	Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)
title_sort	ebstein’s anomaly, left ventricular noncompaction and gerbode-like defect triad (fetal diagnosis and neonatal course)
publisher	Hindawi Limited
publishDate	2021
url	https://doaj.org/article/2c5f683a9368440c89b7387a97a5090d
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Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)

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