Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome

We present a case of 13-year-old female with Turner syndrome (TS), who presented with unexplained lower limbs swelling and ejection systolic murmur at the left second intercostal space. Suspicion of mild aortic coarctation was made by echocardiography. Computed tomography angiography (CTA) showed a...

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Autores principales:	M Obadah Kattea, Osama A Smettei, Abdulrahman Kattea, Rami M Abazid
Formato:	article
Lenguaje:	EN
Publicado:	Thieme Medical and Scientific Publishers Pvt. Ltd. 2016
Materias:	coarctation of aorta interrupted aortic arch left-sided superior vena cava turner syndrome Medicine R
Acceso en línea:	https://doaj.org/article/43f5e64c57b04cb4a76f9e4bb2ffa17f
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spelling	oai:doaj.org-article:43f5e64c57b04cb4a76f9e4bb2ffa17f2021-12-02T17:05:54ZInterrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome2231-07702249-446410.4103/2231-0770.191449https://doaj.org/article/43f5e64c57b04cb4a76f9e4bb2ffa17f2016-10-01T00:00:00Zhttp://www.thieme-connect.de/DOI/DOI?10.4103/2231-0770.191449https://doaj.org/toc/2231-0770https://doaj.org/toc/2249-4464We present a case of 13-year-old female with Turner syndrome (TS), who presented with unexplained lower limbs swelling and ejection systolic murmur at the left second intercostal space. Suspicion of mild aortic coarctation was made by echocardiography. Computed tomography angiography (CTA) showed a complete interruption of the aortic arch (IAA) below the left subclavian artery with persistent left superior vena cava (PLSVC) and absent right SVC, defined as an isolated PLSVC. The patient underwent successful surgical correction after unsuccessful trial of transcatheter stent placement. We present this case of asymptomatic IAA to draw attention to the importance of CTA in diagnosing such rare anomalies and ruling out asymptomatic major cardiovascular abnormalities in patient with TS.M Obadah KatteaOsama A SmetteiAbdulrahman KatteaRami M AbazidThieme Medical and Scientific Publishers Pvt. Ltd.articlecoarctation of aortainterrupted aortic archleft-sided superior vena cavaturner syndromeMedicineRENAvicenna Journal of Medicine, Vol 06, Iss 04, Pp 117-119 (2016)
institution	DOAJ
collection	DOAJ
language	EN
topic	coarctation of aorta interrupted aortic arch left-sided superior vena cava turner syndrome Medicine R
spellingShingle	coarctation of aorta interrupted aortic arch left-sided superior vena cava turner syndrome Medicine R M Obadah Kattea Osama A Smettei Abdulrahman Kattea Rami M Abazid Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome
description	We present a case of 13-year-old female with Turner syndrome (TS), who presented with unexplained lower limbs swelling and ejection systolic murmur at the left second intercostal space. Suspicion of mild aortic coarctation was made by echocardiography. Computed tomography angiography (CTA) showed a complete interruption of the aortic arch (IAA) below the left subclavian artery with persistent left superior vena cava (PLSVC) and absent right SVC, defined as an isolated PLSVC. The patient underwent successful surgical correction after unsuccessful trial of transcatheter stent placement. We present this case of asymptomatic IAA to draw attention to the importance of CTA in diagnosing such rare anomalies and ruling out asymptomatic major cardiovascular abnormalities in patient with TS.
format	article
author	M Obadah Kattea Osama A Smettei Abdulrahman Kattea Rami M Abazid
author_facet	M Obadah Kattea Osama A Smettei Abdulrahman Kattea Rami M Abazid
author_sort	M Obadah Kattea
title	Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome
title_short	Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome
title_full	Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome
title_fullStr	Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome
title_full_unstemmed	Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome
title_sort	interrupted aortic arch with isolated persistent left superior vena cava in patient with turners syndrome
publisher	Thieme Medical and Scientific Publishers Pvt. Ltd.
publishDate	2016
url	https://doaj.org/article/43f5e64c57b04cb4a76f9e4bb2ffa17f
work_keys_str_mv	AT mobadahkattea interruptedaorticarchwithisolatedpersistentleftsuperiorvenacavainpatientwithturnerssyndrome AT osamaasmettei interruptedaorticarchwithisolatedpersistentleftsuperiorvenacavainpatientwithturnerssyndrome AT abdulrahmankattea interruptedaorticarchwithisolatedpersistentleftsuperiorvenacavainpatientwithturnerssyndrome AT ramimabazid interruptedaorticarchwithisolatedpersistentleftsuperiorvenacavainpatientwithturnerssyndrome
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Interrupted aortic arch with isolated persistent left superior vena cava in patient with Turners syndrome

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