Case Report: Evolution of a Severe Vascular Refractory Form of ECD Requiring Liver Transplantation Correlated With the Change in the Monocyte Subset Analysis
Erdheim–Chester disease is a rare histiocytosis characterized by iconic features associated with compatible histology. Most patients have somatic mutations in the MAP-kinase pathway gene, and the mutations occur in CD14+ monocytes. Differentiation of the myeloid lineage plays a central role in the p...
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Autores principales: | Jérôme Razanamahery, Anne Roggy, Jean-François Emile, Alexandre Malakhia, Zaher Lakkis, Francine Garnache-Ottou, Thibaud Soumagne, Fleur Cohen-Aubart, Julien Haroche, Bernard Bonnotte |
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Formato: | article |
Lenguaje: | EN |
Publicado: |
Frontiers Media S.A.
2021
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Materias: | |
Acceso en línea: | https://doaj.org/article/4ee5df62bbbe43378a91e08682975536 |
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