Dorsal intramedullary giant dermoid tumor

Intramedullary dermoid tumors are rare benign neoplasms that correspond to 1 to 2% of all intramedullary tumors, affecting specially the lumbosacral region. Those tumors are composed of remnants of embryonic tissue derived from the ectoderm, whose walls secretions cause slow growth rate. Despite its...

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Autores principales:	Bruna Mendes Lopes Meira, Carla Larissa Cunha Sottomaior, João Gabriel de Melo Silva, Luís Henrique Rossignolli Almeida Prado de Oliveira, Sophia Rodrigues Molina, Ricardo Amoreira Gepp
Formato:	article
Lenguaje:	EN
Publicado:	Brazilian Society for Pediatric Neurosurgery 2021
Materias:	dermoid dermoid cyst intramedullary spinal cord neoplasms giant tumor giant dermoid tumor dorsal intramedullary tumor dermoid tumor Pediatrics RJ1-570 Surgery RD1-811
Acceso en línea:	https://doaj.org/article/53230cd51b91414bbcd0ef352f9136b9
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spelling	oai:doaj.org-article:53230cd51b91414bbcd0ef352f9136b92021-11-23T21:46:36ZDorsal intramedullary giant dermoid tumor2675-362610.46900/apn.v3i3(September-December).52https://doaj.org/article/53230cd51b91414bbcd0ef352f9136b92021-09-01T00:00:00Zhttp://www.archpedneurosurg.com.br/pkp/index.php/sbnped2019/article/view/52https://doaj.org/toc/2675-3626Intramedullary dermoid tumors are rare benign neoplasms that correspond to 1 to 2% of all intramedullary tumors, affecting specially the lumbosacral region. Those tumors are composed of remnants of embryonic tissue derived from the ectoderm, whose walls secretions cause slow growth rate. Despite its benign character, neurological injury comes from the tumor's expansive process and the collateral damage derived from the complete resection of the cyst wall, which can cause hypoesthesia and radicular pain, besides other effects as neuromuscular scoliosis. The primary treatment for intramedullary tumor is resection surgery. The case reported involves an infant with an extensive dorsal intramedullary dermoid tumor without association with spinal dysraphism, presenting clinically complete paraplegia, lower limbs atrophy, hypoesthesia from the T4 level and urinary incontinence. The physical examination revealed upper motor neuron syndrome in the lower limbs, mild cognitive delay and a significant scoliosis. Image exams showed a Cobb angle from T3 to L2 with 115º sitting and 68º with traction, besides a massive expansive intramedullary formation extending from C5 to the T9 plane. The patient underwent extensive cervical and thoracic laminotomy followed by median myelotomy and the resection of the lesion. An arthrodesis treated the secondary vertebral deformity. The postoperative period showed good surgical recovery and the control exams revealed ample resection of the lesion and adequate control of scoliosis with partial maintenance of rotational deformity.Bruna Mendes Lopes MeiraCarla Larissa Cunha SottomaiorJoão Gabriel de Melo SilvaLuís Henrique Rossignolli Almeida Prado de OliveiraSophia Rodrigues MolinaRicardo Amoreira GeppBrazilian Society for Pediatric Neurosurgeryarticledermoiddermoid cystintramedullary spinal cord neoplasmsgiant tumorgiant dermoid tumordorsal intramedullary tumordermoid tumorPediatricsRJ1-570SurgeryRD1-811ENArchives of Pediatric Neurosurgery, Vol 3, Iss 3(September-December), Pp e522021-e522021 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	dermoid dermoid cyst intramedullary spinal cord neoplasms giant tumor giant dermoid tumor dorsal intramedullary tumor dermoid tumor Pediatrics RJ1-570 Surgery RD1-811
spellingShingle	dermoid dermoid cyst intramedullary spinal cord neoplasms giant tumor giant dermoid tumor dorsal intramedullary tumor dermoid tumor Pediatrics RJ1-570 Surgery RD1-811 Bruna Mendes Lopes Meira Carla Larissa Cunha Sottomaior João Gabriel de Melo Silva Luís Henrique Rossignolli Almeida Prado de Oliveira Sophia Rodrigues Molina Ricardo Amoreira Gepp Dorsal intramedullary giant dermoid tumor
description	Intramedullary dermoid tumors are rare benign neoplasms that correspond to 1 to 2% of all intramedullary tumors, affecting specially the lumbosacral region. Those tumors are composed of remnants of embryonic tissue derived from the ectoderm, whose walls secretions cause slow growth rate. Despite its benign character, neurological injury comes from the tumor's expansive process and the collateral damage derived from the complete resection of the cyst wall, which can cause hypoesthesia and radicular pain, besides other effects as neuromuscular scoliosis. The primary treatment for intramedullary tumor is resection surgery. The case reported involves an infant with an extensive dorsal intramedullary dermoid tumor without association with spinal dysraphism, presenting clinically complete paraplegia, lower limbs atrophy, hypoesthesia from the T4 level and urinary incontinence. The physical examination revealed upper motor neuron syndrome in the lower limbs, mild cognitive delay and a significant scoliosis. Image exams showed a Cobb angle from T3 to L2 with 115º sitting and 68º with traction, besides a massive expansive intramedullary formation extending from C5 to the T9 plane. The patient underwent extensive cervical and thoracic laminotomy followed by median myelotomy and the resection of the lesion. An arthrodesis treated the secondary vertebral deformity. The postoperative period showed good surgical recovery and the control exams revealed ample resection of the lesion and adequate control of scoliosis with partial maintenance of rotational deformity.
format	article
author	Bruna Mendes Lopes Meira Carla Larissa Cunha Sottomaior João Gabriel de Melo Silva Luís Henrique Rossignolli Almeida Prado de Oliveira Sophia Rodrigues Molina Ricardo Amoreira Gepp
author_facet	Bruna Mendes Lopes Meira Carla Larissa Cunha Sottomaior João Gabriel de Melo Silva Luís Henrique Rossignolli Almeida Prado de Oliveira Sophia Rodrigues Molina Ricardo Amoreira Gepp
author_sort	Bruna Mendes Lopes Meira
title	Dorsal intramedullary giant dermoid tumor
title_short	Dorsal intramedullary giant dermoid tumor
title_full	Dorsal intramedullary giant dermoid tumor
title_fullStr	Dorsal intramedullary giant dermoid tumor
title_full_unstemmed	Dorsal intramedullary giant dermoid tumor
title_sort	dorsal intramedullary giant dermoid tumor
publisher	Brazilian Society for Pediatric Neurosurgery
publishDate	2021
url	https://doaj.org/article/53230cd51b91414bbcd0ef352f9136b9
work_keys_str_mv	AT brunamendeslopesmeira dorsalintramedullarygiantdermoidtumor AT carlalarissacunhasottomaior dorsalintramedullarygiantdermoidtumor AT joaogabrieldemelosilva dorsalintramedullarygiantdermoidtumor AT luishenriquerossignollialmeidapradodeoliveira dorsalintramedullarygiantdermoidtumor AT sophiarodriguesmolina dorsalintramedullarygiantdermoidtumor AT ricardoamoreiragepp dorsalintramedullarygiantdermoidtumor
_version_	1718416092738617344

Dorsal intramedullary giant dermoid tumor

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