Sudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome

Background. Wolff-Parkinson-White syndrome is an uncommon cardiac disorder characterized by the presence of one or more accessory pathways that predispose patients to frequent episodes of arrhythmias. The prognosis is usually good, but there is a lifetime risk of malignant arrhythmias and sudden car...

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Autores principales: Ana Rita Pereira, Alexandra Briosa, Rita Miranda, Sofia Sequeira Almeida, Luís Brandão, Hélder Pereira
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Publicado: Hindawi Limited 2021
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Acceso en línea:https://doaj.org/article/5821119c7cee45cfa023cf811bc9a0fd
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spelling oai:doaj.org-article:5821119c7cee45cfa023cf811bc9a0fd2021-11-29T00:56:20ZSudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome2090-641210.1155/2021/9083144https://doaj.org/article/5821119c7cee45cfa023cf811bc9a0fd2021-01-01T00:00:00Zhttp://dx.doi.org/10.1155/2021/9083144https://doaj.org/toc/2090-6412Background. Wolff-Parkinson-White syndrome is an uncommon cardiac disorder characterized by the presence of one or more accessory pathways that predispose patients to frequent episodes of arrhythmias. The prognosis is usually good, but there is a lifetime risk of malignant arrhythmias and sudden cardiac death. Case Summary. A 25-year-old male presented a witnessed out-of-hospital cardiac arrest with ventricular fibrillation rhythm. Due to rapid initiation of prehospital advanced life support, return of spontaneous circulation was observed. During the transport to the hospital, an irregular wide complex tachycardia suggestive of preexcited atrial fibrillation with haemodynamic instability was also observed and a synchronized shock was applied. Baseline 12-lead electrocardiogram was compatible with sinus rhythm and ventricular preexcitation pattern. After clinical stabilization, an electrophysiological study was performed confirming the presence of a left anterolateral accessory pathway with a short antegrade effective refractory period. Successful radiofrequency catheter ablation was achieved. Discussion. The reported clinical case recalls fundamental features of the Wolff-Parkinson-White syndrome and outlines the increasing evidence and importance of the invasive risk stratification and even catheter ablation in asymptomatic patients who suffer from this uncommon disease that may have a dramatic and fatal initial clinical manifestation.Ana Rita PereiraAlexandra BriosaRita MirandaSofia Sequeira AlmeidaLuís BrandãoHélder PereiraHindawi LimitedarticleDiseases of the circulatory (Cardiovascular) systemRC666-701ENCase Reports in Cardiology, Vol 2021 (2021)
institution DOAJ
collection DOAJ
language EN
topic Diseases of the circulatory (Cardiovascular) system
RC666-701
spellingShingle Diseases of the circulatory (Cardiovascular) system
RC666-701
Ana Rita Pereira
Alexandra Briosa
Rita Miranda
Sofia Sequeira Almeida
Luís Brandão
Hélder Pereira
Sudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome
description Background. Wolff-Parkinson-White syndrome is an uncommon cardiac disorder characterized by the presence of one or more accessory pathways that predispose patients to frequent episodes of arrhythmias. The prognosis is usually good, but there is a lifetime risk of malignant arrhythmias and sudden cardiac death. Case Summary. A 25-year-old male presented a witnessed out-of-hospital cardiac arrest with ventricular fibrillation rhythm. Due to rapid initiation of prehospital advanced life support, return of spontaneous circulation was observed. During the transport to the hospital, an irregular wide complex tachycardia suggestive of preexcited atrial fibrillation with haemodynamic instability was also observed and a synchronized shock was applied. Baseline 12-lead electrocardiogram was compatible with sinus rhythm and ventricular preexcitation pattern. After clinical stabilization, an electrophysiological study was performed confirming the presence of a left anterolateral accessory pathway with a short antegrade effective refractory period. Successful radiofrequency catheter ablation was achieved. Discussion. The reported clinical case recalls fundamental features of the Wolff-Parkinson-White syndrome and outlines the increasing evidence and importance of the invasive risk stratification and even catheter ablation in asymptomatic patients who suffer from this uncommon disease that may have a dramatic and fatal initial clinical manifestation.
format article
author Ana Rita Pereira
Alexandra Briosa
Rita Miranda
Sofia Sequeira Almeida
Luís Brandão
Hélder Pereira
author_facet Ana Rita Pereira
Alexandra Briosa
Rita Miranda
Sofia Sequeira Almeida
Luís Brandão
Hélder Pereira
author_sort Ana Rita Pereira
title Sudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome
title_short Sudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome
title_full Sudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome
title_fullStr Sudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome
title_full_unstemmed Sudden Cardiac Death: The Most Feared but Potentially Preventable Presentation of Wolff-Parkinson-White Syndrome
title_sort sudden cardiac death: the most feared but potentially preventable presentation of wolff-parkinson-white syndrome
publisher Hindawi Limited
publishDate 2021
url https://doaj.org/article/5821119c7cee45cfa023cf811bc9a0fd
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