Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review

Abstract Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐l...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Tian Luo, Lile Wang, Daiyan Fu, Ruicheng Hu, Chunchu Kong, Yunrong Chen, Xi Li
Formato: article
Lenguaje:EN
Publicado: Wiley 2021
Materias:
Acceso en línea:https://doaj.org/article/58d708caff144c28b9718efae10b9950
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!
Descripción
Sumario:Abstract Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐like pulmonary manifestation. However, such reports are rare in China. We report here a case of GS in China with DPB as the prominent manifestation and carry out a literature review accordingly. Our review indicates that in adults with DPB‐like clinical manifestations, thymic lesions should be excluded and related immune function tests should be performed to exclude GS to avoid missed diagnosis and misdiagnosis.