Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review

Abstract Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐l...

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Autores principales: Tian Luo, Lile Wang, Daiyan Fu, Ruicheng Hu, Chunchu Kong, Yunrong Chen, Xi Li
Formato: article
Lenguaje:EN
Publicado: Wiley 2021
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Acceso en línea:https://doaj.org/article/58d708caff144c28b9718efae10b9950
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spelling oai:doaj.org-article:58d708caff144c28b9718efae10b99502021-11-25T13:46:30ZGood's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review2051-338010.1002/rcr2.873https://doaj.org/article/58d708caff144c28b9718efae10b99502021-12-01T00:00:00Zhttps://doi.org/10.1002/rcr2.873https://doaj.org/toc/2051-3380Abstract Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐like pulmonary manifestation. However, such reports are rare in China. We report here a case of GS in China with DPB as the prominent manifestation and carry out a literature review accordingly. Our review indicates that in adults with DPB‐like clinical manifestations, thymic lesions should be excluded and related immune function tests should be performed to exclude GS to avoid missed diagnosis and misdiagnosis.Tian LuoLile WangDaiyan FuRuicheng HuChunchu KongYunrong ChenXi LiWileyarticlediffuse panbronchiolitisGood's syndromethymomaDiseases of the respiratory systemRC705-779ENRespirology Case Reports, Vol 9, Iss 12, Pp n/a-n/a (2021)
institution DOAJ
collection DOAJ
language EN
topic diffuse panbronchiolitis
Good's syndrome
thymoma
Diseases of the respiratory system
RC705-779
spellingShingle diffuse panbronchiolitis
Good's syndrome
thymoma
Diseases of the respiratory system
RC705-779
Tian Luo
Lile Wang
Daiyan Fu
Ruicheng Hu
Chunchu Kong
Yunrong Chen
Xi Li
Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
description Abstract Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐like pulmonary manifestation. However, such reports are rare in China. We report here a case of GS in China with DPB as the prominent manifestation and carry out a literature review accordingly. Our review indicates that in adults with DPB‐like clinical manifestations, thymic lesions should be excluded and related immune function tests should be performed to exclude GS to avoid missed diagnosis and misdiagnosis.
format article
author Tian Luo
Lile Wang
Daiyan Fu
Ruicheng Hu
Chunchu Kong
Yunrong Chen
Xi Li
author_facet Tian Luo
Lile Wang
Daiyan Fu
Ruicheng Hu
Chunchu Kong
Yunrong Chen
Xi Li
author_sort Tian Luo
title Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_short Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_full Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_fullStr Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_full_unstemmed Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_sort good's syndrome with diffuse panbronchiolitis as the prominent manifestation: a case and literature review
publisher Wiley
publishDate 2021
url https://doaj.org/article/58d708caff144c28b9718efae10b9950
work_keys_str_mv AT tianluo goodssyndromewithdiffusepanbronchiolitisastheprominentmanifestationacaseandliteraturereview
AT lilewang goodssyndromewithdiffusepanbronchiolitisastheprominentmanifestationacaseandliteraturereview
AT daiyanfu goodssyndromewithdiffusepanbronchiolitisastheprominentmanifestationacaseandliteraturereview
AT ruichenghu goodssyndromewithdiffusepanbronchiolitisastheprominentmanifestationacaseandliteraturereview
AT chunchukong goodssyndromewithdiffusepanbronchiolitisastheprominentmanifestationacaseandliteraturereview
AT yunrongchen goodssyndromewithdiffusepanbronchiolitisastheprominentmanifestationacaseandliteraturereview
AT xili goodssyndromewithdiffusepanbronchiolitisastheprominentmanifestationacaseandliteraturereview
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