Primary Ewings sarcoma in liver - A rare case report with review of literature

Ewing's sarcoma family of tumours include both peripheral primitive neuroectodermal tumour (PNET) and Ewing's sarcoma including both intraosseous and extra osseous sites. Rarest of all is the involvement of liver as primary site, of which only 4 case reports have been published. We report...

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Autores principales:	Anjali Sharma, Neha Sethi, Shashikant Saini, Kirti Pandia, Ritu Jangir
Formato:	article
Lenguaje:	EN
Publicado:	Wolters Kluwer Medknow Publications 2021
Materias:	ewings fli 1 liver pnet Pathology RB1-214 Microbiology QR1-502
Acceso en línea:	https://doaj.org/article/58f0aae9249e430db37d3b5686b30fee
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spelling	oai:doaj.org-article:58f0aae9249e430db37d3b5686b30fee2021-12-02T17:28:22ZPrimary Ewings sarcoma in liver - A rare case report with review of literature0377-492910.4103/IJPM.IJPM_288_19https://doaj.org/article/58f0aae9249e430db37d3b5686b30fee2021-01-01T00:00:00Zhttp://www.ijpmonline.org/article.asp?issn=0377-4929;year=2021;volume=64;issue=5;spage=136;epage=139;aulast=Sharmahttps://doaj.org/toc/0377-4929Ewing's sarcoma family of tumours include both peripheral primitive neuroectodermal tumour (PNET) and Ewing's sarcoma including both intraosseous and extra osseous sites. Rarest of all is the involvement of liver as primary site, of which only 4 case reports have been published. We report a very rare case of 4 year old male child with primary Ewing's Sarcoma in the liver along with review of literature. The child presented with pain abdomen and low grade fever and hepatomegaly. On putting extensive IHC panel on liver SOL biopsy the small round cells were positive for FLI-1 & CD99 & were immunonegative for OCH, LCA, AFP, WT1, NSE, MYOGENIN, B-catenin & glypican 3. The histopathological and immunohistochemical profile was suggestive of Ewing's Sarcoma. To our knowledge, this is the fifth reported case of Ewing's Sarcoma occurring in liver as primary & first case to be present in a young boy of 4 years age.Anjali SharmaNeha SethiShashikant SainiKirti PandiaRitu JangirWolters Kluwer Medknow Publicationsarticleewingsfli 1liverpnetPathologyRB1-214MicrobiologyQR1-502ENIndian Journal of Pathology and Microbiology, Vol 64, Iss 5, Pp 136-139 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	ewings fli 1 liver pnet Pathology RB1-214 Microbiology QR1-502
spellingShingle	ewings fli 1 liver pnet Pathology RB1-214 Microbiology QR1-502 Anjali Sharma Neha Sethi Shashikant Saini Kirti Pandia Ritu Jangir Primary Ewings sarcoma in liver - A rare case report with review of literature
description	Ewing's sarcoma family of tumours include both peripheral primitive neuroectodermal tumour (PNET) and Ewing's sarcoma including both intraosseous and extra osseous sites. Rarest of all is the involvement of liver as primary site, of which only 4 case reports have been published. We report a very rare case of 4 year old male child with primary Ewing's Sarcoma in the liver along with review of literature. The child presented with pain abdomen and low grade fever and hepatomegaly. On putting extensive IHC panel on liver SOL biopsy the small round cells were positive for FLI-1 & CD99 & were immunonegative for OCH, LCA, AFP, WT1, NSE, MYOGENIN, B-catenin & glypican 3. The histopathological and immunohistochemical profile was suggestive of Ewing's Sarcoma. To our knowledge, this is the fifth reported case of Ewing's Sarcoma occurring in liver as primary & first case to be present in a young boy of 4 years age.
format	article
author	Anjali Sharma Neha Sethi Shashikant Saini Kirti Pandia Ritu Jangir
author_facet	Anjali Sharma Neha Sethi Shashikant Saini Kirti Pandia Ritu Jangir
author_sort	Anjali Sharma
title	Primary Ewings sarcoma in liver - A rare case report with review of literature
title_short	Primary Ewings sarcoma in liver - A rare case report with review of literature
title_full	Primary Ewings sarcoma in liver - A rare case report with review of literature
title_fullStr	Primary Ewings sarcoma in liver - A rare case report with review of literature
title_full_unstemmed	Primary Ewings sarcoma in liver - A rare case report with review of literature
title_sort	primary ewings sarcoma in liver - a rare case report with review of literature
publisher	Wolters Kluwer Medknow Publications
publishDate	2021
url	https://doaj.org/article/58f0aae9249e430db37d3b5686b30fee
work_keys_str_mv	AT anjalisharma primaryewingssarcomainliverararecasereportwithreviewofliterature AT nehasethi primaryewingssarcomainliverararecasereportwithreviewofliterature AT shashikantsaini primaryewingssarcomainliverararecasereportwithreviewofliterature AT kirtipandia primaryewingssarcomainliverararecasereportwithreviewofliterature AT ritujangir primaryewingssarcomainliverararecasereportwithreviewofliterature
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Primary Ewings sarcoma in liver - A rare case report with review of literature

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