Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report

Macrophage activation syndrome is a rare but a life threatening condition commonly associated with Systemic Juvenile Idiopathic Arthritis. Its clinical presentation includes fever, hepatosplenomegaly, hypertriglyceridemia, hypofibrinogenemia, hyperferritinemia and impaired liver enzymes. The sympto...

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Autores principales:	Rishikesh Kafle, Anwesh Bhatta, Sumit Gami, Abhin Sapkota, Dipesh Sharma, Arabindra Yadav, Vijaya Kumar Chikanbanjar
Formato:	article
Lenguaje:	EN
Publicado:	Nepal Medical Association 2021
Materias:	juvenile arthritis; macrophage activation syndrome; steroids. Medicine (General) R5-920
Acceso en línea:	https://doaj.org/article/5d5177583b094c38bac25c8390c4ecc8
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spelling	oai:doaj.org-article:5d5177583b094c38bac25c8390c4ecc82021-11-18T19:20:03ZMacrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report10.31729/jnma.70190028-27151815-672Xhttps://doaj.org/article/5d5177583b094c38bac25c8390c4ecc82021-11-01T00:00:00Zhttp://www.jnma.com.np/jnma/index.php/jnma/article/view/7019https://doaj.org/toc/0028-2715https://doaj.org/toc/1815-672X Macrophage activation syndrome is a rare but a life threatening condition commonly associated with Systemic Juvenile Idiopathic Arthritis. Its clinical presentation includes fever, hepatosplenomegaly, hypertriglyceridemia, hypofibrinogenemia, hyperferritinemia and impaired liver enzymes. The symptoms are alarming yet non-specific and often lead to a delayed diagnosis. A 12 year male presented with a history of intermittent fever and was started on antibiotics but failed to respond after several days of hospital stay. After a series of investigations to rule out multiple diagnoses he was diagnosed as a case of Macrophage Activation Syndrome secondary to Systemic onset Juvenile Arthritis and was treated with steroids. Rishikesh KafleAnwesh BhattaSumit GamiAbhin SapkotaDipesh SharmaArabindra YadavVijaya Kumar ChikanbanjarNepal Medical Associationarticlejuvenile arthritis; macrophage activation syndrome; steroids.Medicine (General)R5-920ENJournal of Nepal Medical Association, Vol 59, Iss 243 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	juvenile arthritis; macrophage activation syndrome; steroids. Medicine (General) R5-920
spellingShingle	juvenile arthritis; macrophage activation syndrome; steroids. Medicine (General) R5-920 Rishikesh Kafle Anwesh Bhatta Sumit Gami Abhin Sapkota Dipesh Sharma Arabindra Yadav Vijaya Kumar Chikanbanjar Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report
description	Macrophage activation syndrome is a rare but a life threatening condition commonly associated with Systemic Juvenile Idiopathic Arthritis. Its clinical presentation includes fever, hepatosplenomegaly, hypertriglyceridemia, hypofibrinogenemia, hyperferritinemia and impaired liver enzymes. The symptoms are alarming yet non-specific and often lead to a delayed diagnosis. A 12 year male presented with a history of intermittent fever and was started on antibiotics but failed to respond after several days of hospital stay. After a series of investigations to rule out multiple diagnoses he was diagnosed as a case of Macrophage Activation Syndrome secondary to Systemic onset Juvenile Arthritis and was treated with steroids.
format	article
author	Rishikesh Kafle Anwesh Bhatta Sumit Gami Abhin Sapkota Dipesh Sharma Arabindra Yadav Vijaya Kumar Chikanbanjar
author_facet	Rishikesh Kafle Anwesh Bhatta Sumit Gami Abhin Sapkota Dipesh Sharma Arabindra Yadav Vijaya Kumar Chikanbanjar
author_sort	Rishikesh Kafle
title	Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report
title_short	Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report
title_full	Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report
title_fullStr	Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report
title_full_unstemmed	Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report
title_sort	macrophage activation syndrome secondary to systemic juvenile idiopathic arthritis: a case report
publisher	Nepal Medical Association
publishDate	2021
url	https://doaj.org/article/5d5177583b094c38bac25c8390c4ecc8
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Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report

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