A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject

CPC is a rare reginal variant as per international Krickenbeck classification, in which colon (partly or complete) is replaced by a pouch like dilatation, opening into urogenital tract via a large fistula. Theassociation of CPC without a fistula with ARM is very rare. Type I: Absent large colon, wit...

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Autores principales:	Parveen Kumar, Rishabh Jain, Arti Khatri
Formato:	article
Lenguaje:	EN
Publicado:	Shiraz University of Medical Sciences 2019
Materias:	cpc (congenital pouch colon) arm (anorectal malformation) fistula Medicine R
Acceso en línea:	https://doaj.org/article/617ae164a621476a9911dd8f6f0b9636
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spelling	oai:doaj.org-article:617ae164a621476a9911dd8f6f0b96362021-11-14T08:42:24ZA Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject2783-2430https://doaj.org/article/617ae164a621476a9911dd8f6f0b96362019-09-01T00:00:00Zhttps://colorectalresearch.sums.ac.ir/article_45861_e324ca93579167b15e295eb782c78acc.pdfhttps://doaj.org/toc/2783-2430CPC is a rare reginal variant as per international Krickenbeck classification, in which colon (partly or complete) is replaced by a pouch like dilatation, opening into urogenital tract via a large fistula. Theassociation of CPC without a fistula with ARM is very rare. Type I: Absent large colon, with ileum opening directly into pouch. Type II: The presence of short segment of caecum which then opens into pouch. Type III: The presence of good length of colon between ileum and pouch. Type IV: The presence of large colon with only sigmoid and rectum converted into pouch A 2-day-old female baby presented with radiological features of pouch colon, which intra-operatively revealed type 4 CPC without fistula. The vestibule had two normal openings, with an external anal marking in perineum with puckering of skin but without any caliber. She underwent excision of pouch with end stoma and awaiting abdomino-perineal pull through at 6 months of age. To best of our knowledge, there is no case reported of CPC without fistula with external anal marking and puckering.Parveen KumarRishabh JainArti KhatriShiraz University of Medical Sciencesarticlecpc (congenital pouch colon)arm (anorectal malformation)fistulaMedicineRENIranian Journal of Colorectal Research, Vol 7, Iss 3, Pp 1-3 (2019)
institution	DOAJ
collection	DOAJ
language	EN
topic	cpc (congenital pouch colon) arm (anorectal malformation) fistula Medicine R
spellingShingle	cpc (congenital pouch colon) arm (anorectal malformation) fistula Medicine R Parveen Kumar Rishabh Jain Arti Khatri A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject
description	CPC is a rare reginal variant as per international Krickenbeck classification, in which colon (partly or complete) is replaced by a pouch like dilatation, opening into urogenital tract via a large fistula. Theassociation of CPC without a fistula with ARM is very rare. Type I: Absent large colon, with ileum opening directly into pouch. Type II: The presence of short segment of caecum which then opens into pouch. Type III: The presence of good length of colon between ileum and pouch. Type IV: The presence of large colon with only sigmoid and rectum converted into pouch A 2-day-old female baby presented with radiological features of pouch colon, which intra-operatively revealed type 4 CPC without fistula. The vestibule had two normal openings, with an external anal marking in perineum with puckering of skin but without any caliber. She underwent excision of pouch with end stoma and awaiting abdomino-perineal pull through at 6 months of age. To best of our knowledge, there is no case reported of CPC without fistula with external anal marking and puckering.
format	article
author	Parveen Kumar Rishabh Jain Arti Khatri
author_facet	Parveen Kumar Rishabh Jain Arti Khatri
author_sort	Parveen Kumar
title	A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject
title_short	A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject
title_full	A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject
title_fullStr	A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject
title_full_unstemmed	A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject
title_sort	rare case of type 4 congenital pouch colon without fistula with external anal marking in a female subject
publisher	Shiraz University of Medical Sciences
publishDate	2019
url	https://doaj.org/article/617ae164a621476a9911dd8f6f0b9636
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A Rare case of Type 4 Congenital Pouch colon without fistula with external anal marking in a female subject

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