Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria

Orbital rhabdomyosarcoma (RMS) is a highly malignant tumor that originates mainly from mesenchymal tissue. It is considered a rare childhood malignancy; therefore, presentation in adulthood is scarce. In this case report, a 36-year-old male patient presented with a rapidly progressive RMS of the lef...

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Autores principales:	Tagrid Younes Ahmad, Hasan Nabil Al Houri, Abdullah Nabil Al Houri, Nagham Younes Ahmad
Formato:	article
Lenguaje:	EN
Publicado:	Thieme Medical and Scientific Publishers Pvt. Ltd. 2018
Materias:	adulthood oncology ophthalmology orbital rhabdomyosarcoma Medicine R
Acceso en línea:	https://doaj.org/article/6ae093a9272f413bae66f433c7be28a5
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spelling	oai:doaj.org-article:6ae093a9272f413bae66f433c7be28a52021-12-02T18:50:08ZAggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria2231-07702249-446410.4103/ajm.AJM_62_18https://doaj.org/article/6ae093a9272f413bae66f433c7be28a52018-07-01T00:00:00Zhttp://www.thieme-connect.de/DOI/DOI?10.4103/ajm.AJM_62_18https://doaj.org/toc/2231-0770https://doaj.org/toc/2249-4464Orbital rhabdomyosarcoma (RMS) is a highly malignant tumor that originates mainly from mesenchymal tissue. It is considered a rare childhood malignancy; therefore, presentation in adulthood is scarce. In this case report, a 36-year-old male patient presented with a rapidly progressive RMS of the left orbit. The patient was treated in a different institution with radiochemotherapy with good response. However, relapse occurred after 2 months of completing the course, as rapid growing proptosis. Computed tomography scan revealed a lesion in the left orbit with invasion of the left ethmoid cells and the left maxillary sinus. Exenteration of the left orbit with the left partial maxillectomy and ethmoidectomy was performed. RMS is a highly aggressive malignancy that should be considered in any orbital mass that progresses rapidly. Surgery should be the first line in treatment. Delay in diagnosis and inappropriate treatment negatively affects the outcome.Tagrid Younes AhmadHasan Nabil Al HouriAbdullah Nabil Al HouriNagham Younes AhmadThieme Medical and Scientific Publishers Pvt. Ltd.articleadulthoodoncologyophthalmologyorbital rhabdomyosarcomaMedicineRENAvicenna Journal of Medicine, Vol 8, Iss 03, Pp 110-113 (2018)
institution	DOAJ
collection	DOAJ
language	EN
topic	adulthood oncology ophthalmology orbital rhabdomyosarcoma Medicine R
spellingShingle	adulthood oncology ophthalmology orbital rhabdomyosarcoma Medicine R Tagrid Younes Ahmad Hasan Nabil Al Houri Abdullah Nabil Al Houri Nagham Younes Ahmad Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria
description	Orbital rhabdomyosarcoma (RMS) is a highly malignant tumor that originates mainly from mesenchymal tissue. It is considered a rare childhood malignancy; therefore, presentation in adulthood is scarce. In this case report, a 36-year-old male patient presented with a rapidly progressive RMS of the left orbit. The patient was treated in a different institution with radiochemotherapy with good response. However, relapse occurred after 2 months of completing the course, as rapid growing proptosis. Computed tomography scan revealed a lesion in the left orbit with invasion of the left ethmoid cells and the left maxillary sinus. Exenteration of the left orbit with the left partial maxillectomy and ethmoidectomy was performed. RMS is a highly aggressive malignancy that should be considered in any orbital mass that progresses rapidly. Surgery should be the first line in treatment. Delay in diagnosis and inappropriate treatment negatively affects the outcome.
format	article
author	Tagrid Younes Ahmad Hasan Nabil Al Houri Abdullah Nabil Al Houri Nagham Younes Ahmad
author_facet	Tagrid Younes Ahmad Hasan Nabil Al Houri Abdullah Nabil Al Houri Nagham Younes Ahmad
author_sort	Tagrid Younes Ahmad
title	Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria
title_short	Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria
title_full	Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria
title_fullStr	Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria
title_full_unstemmed	Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria
title_sort	aggressive orbital rhabdomyosarcoma in adulthood: a case report in a public hospital in damascus, syria
publisher	Thieme Medical and Scientific Publishers Pvt. Ltd.
publishDate	2018
url	https://doaj.org/article/6ae093a9272f413bae66f433c7be28a5
work_keys_str_mv	AT tagridyounesahmad aggressiveorbitalrhabdomyosarcomainadulthoodacasereportinapublichospitalindamascussyria AT hasannabilalhouri aggressiveorbitalrhabdomyosarcomainadulthoodacasereportinapublichospitalindamascussyria AT abdullahnabilalhouri aggressiveorbitalrhabdomyosarcomainadulthoodacasereportinapublichospitalindamascussyria AT naghamyounesahmad aggressiveorbitalrhabdomyosarcomainadulthoodacasereportinapublichospitalindamascussyria
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Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria

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