Idiopathic noncirrhotic portal hypertension: current perspectives

Oliviero Riggio,1 Stefania Gioia,1 Ilaria Pentassuglio,1 Valeria Nicoletti,1 Michele Valente,2 Giulia d’Amati2 1Department of Clinical Medicine, Center for the Diagnosis and Treatment of Portal Hypertension, 2Department of Radiological, Oncological, and Pathological Sciences, Sapienza Univ...

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Autores principales:	Riggio O, Gioia S, Pentassuglio I, Nicoletti V, Valente M, d’Amati G
Formato:	article
Lenguaje:	EN
Publicado:	Dove Medical Press 2016
Materias:	Idiopathic portal hypertension Obliterative portal venopathy Oesophageal varices Splenomegaly Diseases of the digestive system. Gastroenterology RC799-869
Acceso en línea:	https://doaj.org/article/71e285cd3d264da59b5cc8a0ba39e4d5
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spelling	oai:doaj.org-article:71e285cd3d264da59b5cc8a0ba39e4d52021-12-02T03:26:49ZIdiopathic noncirrhotic portal hypertension: current perspectives1179-1535https://doaj.org/article/71e285cd3d264da59b5cc8a0ba39e4d52016-07-01T00:00:00Zhttps://www.dovepress.com/idiopathic-noncirrhotic-portal-hypertension-current-perspectives-peer-reviewed-article-HMERhttps://doaj.org/toc/1179-1535Oliviero Riggio,1 Stefania Gioia,1 Ilaria Pentassuglio,1 Valeria Nicoletti,1 Michele Valente,2 Giulia d’Amati2 1Department of Clinical Medicine, Center for the Diagnosis and Treatment of Portal Hypertension, 2Department of Radiological, Oncological, and Pathological Sciences, Sapienza University of Rome, Rome, Italy Abstract: The term idiopathic noncirrhotic portal hypertension (INCPH) has been recently proposed to replace terms, such as hepatoportal sclerosis, idiopathic portal hypertension, incomplete septal cirrhosis, and nodular regenerative hyperplasia, used to describe patients with a hepatic presinusoidal cause of portal hypertension of unknown etiology, characterized by features of portal hypertension (esophageal varices, nonmalignant ascites, porto-venous collaterals), splenomegaly, patent portal, and hepatic veins and no clinical and histological signs of cirrhosis. Physicians should learn to look for this condition in a number of clinical settings, including cryptogenic cirrhosis, a disease known to be associated with INCPH, drug administration, and even chronic alterations in liver function tests. Once INCPH is clinically suspected, liver histology becomes mandatory for the correct diagnosis. However, pathologists should be familiar with the histological features of INCPH, especially in cases in which histology is not only requested to exclude liver cirrhosis. Keywords: idiopathic portal hypertension, obliterative portal venopathy, esophageal varices, splenomegalyRiggio OGioia SPentassuglio INicoletti VValente Md’Amati GDove Medical PressarticleIdiopathic portal hypertensionObliterative portal venopathyOesophageal varicesSplenomegalyDiseases of the digestive system. GastroenterologyRC799-869ENHepatic Medicine: Evidence and Research, Vol 2016, Iss Issue 1, Pp 81-88 (2016)
institution	DOAJ
collection	DOAJ
language	EN
topic	Idiopathic portal hypertension Obliterative portal venopathy Oesophageal varices Splenomegaly Diseases of the digestive system. Gastroenterology RC799-869
spellingShingle	Idiopathic portal hypertension Obliterative portal venopathy Oesophageal varices Splenomegaly Diseases of the digestive system. Gastroenterology RC799-869 Riggio O Gioia S Pentassuglio I Nicoletti V Valente M d’Amati G Idiopathic noncirrhotic portal hypertension: current perspectives
description	Oliviero Riggio,1 Stefania Gioia,1 Ilaria Pentassuglio,1 Valeria Nicoletti,1 Michele Valente,2 Giulia d’Amati2 1Department of Clinical Medicine, Center for the Diagnosis and Treatment of Portal Hypertension, 2Department of Radiological, Oncological, and Pathological Sciences, Sapienza University of Rome, Rome, Italy Abstract: The term idiopathic noncirrhotic portal hypertension (INCPH) has been recently proposed to replace terms, such as hepatoportal sclerosis, idiopathic portal hypertension, incomplete septal cirrhosis, and nodular regenerative hyperplasia, used to describe patients with a hepatic presinusoidal cause of portal hypertension of unknown etiology, characterized by features of portal hypertension (esophageal varices, nonmalignant ascites, porto-venous collaterals), splenomegaly, patent portal, and hepatic veins and no clinical and histological signs of cirrhosis. Physicians should learn to look for this condition in a number of clinical settings, including cryptogenic cirrhosis, a disease known to be associated with INCPH, drug administration, and even chronic alterations in liver function tests. Once INCPH is clinically suspected, liver histology becomes mandatory for the correct diagnosis. However, pathologists should be familiar with the histological features of INCPH, especially in cases in which histology is not only requested to exclude liver cirrhosis. Keywords: idiopathic portal hypertension, obliterative portal venopathy, esophageal varices, splenomegaly
format	article
author	Riggio O Gioia S Pentassuglio I Nicoletti V Valente M d’Amati G
author_facet	Riggio O Gioia S Pentassuglio I Nicoletti V Valente M d’Amati G
author_sort	Riggio O
title	Idiopathic noncirrhotic portal hypertension: current perspectives
title_short	Idiopathic noncirrhotic portal hypertension: current perspectives
title_full	Idiopathic noncirrhotic portal hypertension: current perspectives
title_fullStr	Idiopathic noncirrhotic portal hypertension: current perspectives
title_full_unstemmed	Idiopathic noncirrhotic portal hypertension: current perspectives
title_sort	idiopathic noncirrhotic portal hypertension: current perspectives
publisher	Dove Medical Press
publishDate	2016
url	https://doaj.org/article/71e285cd3d264da59b5cc8a0ba39e4d5
work_keys_str_mv	AT riggioo idiopathicnoncirrhoticportalhypertensioncurrentperspectives AT gioias idiopathicnoncirrhoticportalhypertensioncurrentperspectives AT pentassuglioi idiopathicnoncirrhoticportalhypertensioncurrentperspectives AT nicolettiv idiopathicnoncirrhoticportalhypertensioncurrentperspectives AT valentem idiopathicnoncirrhoticportalhypertensioncurrentperspectives AT damatig idiopathicnoncirrhoticportalhypertensioncurrentperspectives
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Idiopathic noncirrhotic portal hypertension: current perspectives

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