Progressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation
Moyamoya disease is a chronic and unusual cerebrovascular disorder characterized by progressive stenosis and occlusion of the distal portions of internal carotid arteries and its main branches within the circle of Willis. Posterior circulation (vertebral and basilar arteries) may also be affected; h...
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2017
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oai:doaj.org-article:8912e9221b934b29aa4999525657972b2021-11-03T23:45:46ZProgressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation0103-53552359-592210.1055/s-0037-1602378https://doaj.org/article/8912e9221b934b29aa4999525657972b2017-04-01T00:00:00Zhttp://www.thieme-connect.de/DOI/DOI?10.1055/s-0037-1602378https://doaj.org/toc/0103-5355https://doaj.org/toc/2359-5922Moyamoya disease is a chronic and unusual cerebrovascular disorder characterized by progressive stenosis and occlusion of the distal portions of internal carotid arteries and its main branches within the circle of Willis. Posterior circulation (vertebral and basilar arteries) may also be affected; however, this presentation is uncommon. As well as stenosis of the terminal portion of intracranial arteries, it is seen the development of a network of collateral vessels abnormally dilated at the base of the brain with an aspect of a “puff of smoke,” whose term in Japanese is described as “moyamoya.” The present study aims to report two consecutive cases of patients who presented to our service with different clinical manifestations. Further investigation with digital subtraction angiography showed a moyamoya pattern.Marx Lima de Barros-AraújoTibério Silva Borges dos SantosIrapuá Ferreira RicarteGuilherme Victor Sousa MedeirosJoemir Jabson da Conceição BritoStephany Vargas GuindaniLarissa Clementino Leite de Sá CarvalhoThieme Revinter Publicações Ltda.articlecerebral arteriopathyprogressive vasculopathymoyamoyaMedicineRSurgeryRD1-811ENBrazilian Neurosurgery, Vol 40, Iss 03, Pp e272-e276 (2017) |
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cerebral arteriopathy progressive vasculopathy moyamoya Medicine R Surgery RD1-811 |
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cerebral arteriopathy progressive vasculopathy moyamoya Medicine R Surgery RD1-811 Marx Lima de Barros-Araújo Tibério Silva Borges dos Santos Irapuá Ferreira Ricarte Guilherme Victor Sousa Medeiros Joemir Jabson da Conceição Brito Stephany Vargas Guindani Larissa Clementino Leite de Sá Carvalho Progressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation |
description |
Moyamoya disease is a chronic and unusual cerebrovascular disorder characterized by progressive stenosis and occlusion of the distal portions of internal carotid arteries and its main branches within the circle of Willis. Posterior circulation (vertebral and basilar arteries) may also be affected; however, this presentation is uncommon. As well as stenosis of the terminal portion of intracranial arteries, it is seen the development of a network of collateral vessels abnormally dilated at the base of the brain with an aspect of a “puff of smoke,” whose term in Japanese is described as “moyamoya.” The present study aims to report two consecutive cases of patients who presented to our service with different clinical manifestations. Further investigation with digital subtraction angiography showed a moyamoya pattern. |
format |
article |
author |
Marx Lima de Barros-Araújo Tibério Silva Borges dos Santos Irapuá Ferreira Ricarte Guilherme Victor Sousa Medeiros Joemir Jabson da Conceição Brito Stephany Vargas Guindani Larissa Clementino Leite de Sá Carvalho |
author_facet |
Marx Lima de Barros-Araújo Tibério Silva Borges dos Santos Irapuá Ferreira Ricarte Guilherme Victor Sousa Medeiros Joemir Jabson da Conceição Brito Stephany Vargas Guindani Larissa Clementino Leite de Sá Carvalho |
author_sort |
Marx Lima de Barros-Araújo |
title |
Progressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation |
title_short |
Progressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation |
title_full |
Progressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation |
title_fullStr |
Progressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation |
title_full_unstemmed |
Progressive Cerebral Arteriopathy – Moyamoya Disease: A Report of Two Cases with Different Clinical Presentation |
title_sort |
progressive cerebral arteriopathy – moyamoya disease: a report of two cases with different clinical presentation |
publisher |
Thieme Revinter Publicações Ltda. |
publishDate |
2017 |
url |
https://doaj.org/article/8912e9221b934b29aa4999525657972b |
work_keys_str_mv |
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