Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often...
Guardado en:
Autores principales: | , , , , , |
---|---|
Formato: | article |
Lenguaje: | EN |
Publicado: |
Elsevier
2022
|
Materias: | |
Acceso en línea: | https://doaj.org/article/979482b0c26b4674a9e890ffde928155 |
Etiquetas: |
Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!
|
id |
oai:doaj.org-article:979482b0c26b4674a9e890ffde928155 |
---|---|
record_format |
dspace |
spelling |
oai:doaj.org-article:979482b0c26b4674a9e890ffde9281552021-11-30T04:15:18ZPulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report1930-043310.1016/j.radcr.2021.10.033https://doaj.org/article/979482b0c26b4674a9e890ffde9281552022-01-01T00:00:00Zhttp://www.sciencedirect.com/science/article/pii/S1930043321007494https://doaj.org/toc/1930-0433Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often occurs secondary to acute cardiac tamponade, as the pulmonary artery dissects into the pericardium; this diagnosis is often made postmortem. Nevertheless, with the proliferation of multidetector computed tomography (MDCT) as a diagnostic test, patients may be identified very early after symptom onset, prompting rapid intervention with decreased morbidity and mortality. We report a case of IPAH complicated by pulmonary artery aneurysm (PAA) and PAD, diagnosed by CT pulmonary angiogram (CTPA), and treated with bilateral lung transplantation, pulmonic valve replacement, and re-anastomosis of the donor main PA to a pulmonary valve conduit.Luis Regalado, BS, MScCarol Vitellas, BALindsay Wright, MDAsvin Ganapathi, MDBryan A. Whitson, MD, PhDChiemezie Chianotu Amadi, MD, MAElsevierarticlePulmonary hypertensionPulmonary artery aneurysmPulmonary arterial hypertensionIdiopathic pulmonary arterial hypertensionPulmonary artery dissectionLung transplantationMedical physics. Medical radiology. Nuclear medicineR895-920ENRadiology Case Reports, Vol 17, Iss 1, Pp 227-231 (2022) |
institution |
DOAJ |
collection |
DOAJ |
language |
EN |
topic |
Pulmonary hypertension Pulmonary artery aneurysm Pulmonary arterial hypertension Idiopathic pulmonary arterial hypertension Pulmonary artery dissection Lung transplantation Medical physics. Medical radiology. Nuclear medicine R895-920 |
spellingShingle |
Pulmonary hypertension Pulmonary artery aneurysm Pulmonary arterial hypertension Idiopathic pulmonary arterial hypertension Pulmonary artery dissection Lung transplantation Medical physics. Medical radiology. Nuclear medicine R895-920 Luis Regalado, BS, MSc Carol Vitellas, BA Lindsay Wright, MD Asvin Ganapathi, MD Bryan A. Whitson, MD, PhD Chiemezie Chianotu Amadi, MD, MA Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
description |
Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often occurs secondary to acute cardiac tamponade, as the pulmonary artery dissects into the pericardium; this diagnosis is often made postmortem. Nevertheless, with the proliferation of multidetector computed tomography (MDCT) as a diagnostic test, patients may be identified very early after symptom onset, prompting rapid intervention with decreased morbidity and mortality. We report a case of IPAH complicated by pulmonary artery aneurysm (PAA) and PAD, diagnosed by CT pulmonary angiogram (CTPA), and treated with bilateral lung transplantation, pulmonic valve replacement, and re-anastomosis of the donor main PA to a pulmonary valve conduit. |
format |
article |
author |
Luis Regalado, BS, MSc Carol Vitellas, BA Lindsay Wright, MD Asvin Ganapathi, MD Bryan A. Whitson, MD, PhD Chiemezie Chianotu Amadi, MD, MA |
author_facet |
Luis Regalado, BS, MSc Carol Vitellas, BA Lindsay Wright, MD Asvin Ganapathi, MD Bryan A. Whitson, MD, PhD Chiemezie Chianotu Amadi, MD, MA |
author_sort |
Luis Regalado, BS, MSc |
title |
Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
title_short |
Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
title_full |
Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
title_fullStr |
Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
title_full_unstemmed |
Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
title_sort |
pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: a case report |
publisher |
Elsevier |
publishDate |
2022 |
url |
https://doaj.org/article/979482b0c26b4674a9e890ffde928155 |
work_keys_str_mv |
AT luisregaladobsmsc pulmonaryarterydissectioninlongstandingidiopathicpulmonaryarterialhypertensionacasereport AT carolvitellasba pulmonaryarterydissectioninlongstandingidiopathicpulmonaryarterialhypertensionacasereport AT lindsaywrightmd pulmonaryarterydissectioninlongstandingidiopathicpulmonaryarterialhypertensionacasereport AT asvinganapathimd pulmonaryarterydissectioninlongstandingidiopathicpulmonaryarterialhypertensionacasereport AT bryanawhitsonmdphd pulmonaryarterydissectioninlongstandingidiopathicpulmonaryarterialhypertensionacasereport AT chiemeziechianotuamadimdma pulmonaryarterydissectioninlongstandingidiopathicpulmonaryarterialhypertensionacasereport |
_version_ |
1718406820790272000 |