Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report

Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often...

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Autores principales: Luis Regalado, BS, MSc, Carol Vitellas, BA, Lindsay Wright, MD, Asvin Ganapathi, MD, Bryan A. Whitson, MD, PhD, Chiemezie Chianotu Amadi, MD, MA
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Publicado: Elsevier 2022
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Acceso en línea:https://doaj.org/article/979482b0c26b4674a9e890ffde928155
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spelling oai:doaj.org-article:979482b0c26b4674a9e890ffde9281552021-11-30T04:15:18ZPulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report1930-043310.1016/j.radcr.2021.10.033https://doaj.org/article/979482b0c26b4674a9e890ffde9281552022-01-01T00:00:00Zhttp://www.sciencedirect.com/science/article/pii/S1930043321007494https://doaj.org/toc/1930-0433Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often occurs secondary to acute cardiac tamponade, as the pulmonary artery dissects into the pericardium; this diagnosis is often made postmortem. Nevertheless, with the proliferation of multidetector computed tomography (MDCT) as a diagnostic test, patients may be identified very early after symptom onset, prompting rapid intervention with decreased morbidity and mortality. We report a case of IPAH complicated by pulmonary artery aneurysm (PAA) and PAD, diagnosed by CT pulmonary angiogram (CTPA), and treated with bilateral lung transplantation, pulmonic valve replacement, and re-anastomosis of the donor main PA to a pulmonary valve conduit.Luis Regalado, BS, MScCarol Vitellas, BALindsay Wright, MDAsvin Ganapathi, MDBryan A. Whitson, MD, PhDChiemezie Chianotu Amadi, MD, MAElsevierarticlePulmonary hypertensionPulmonary artery aneurysmPulmonary arterial hypertensionIdiopathic pulmonary arterial hypertensionPulmonary artery dissectionLung transplantationMedical physics. Medical radiology. Nuclear medicineR895-920ENRadiology Case Reports, Vol 17, Iss 1, Pp 227-231 (2022)
institution DOAJ
collection DOAJ
language EN
topic Pulmonary hypertension
Pulmonary artery aneurysm
Pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Pulmonary artery dissection
Lung transplantation
Medical physics. Medical radiology. Nuclear medicine
R895-920
spellingShingle Pulmonary hypertension
Pulmonary artery aneurysm
Pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Pulmonary artery dissection
Lung transplantation
Medical physics. Medical radiology. Nuclear medicine
R895-920
Luis Regalado, BS, MSc
Carol Vitellas, BA
Lindsay Wright, MD
Asvin Ganapathi, MD
Bryan A. Whitson, MD, PhD
Chiemezie Chianotu Amadi, MD, MA
Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
description Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often occurs secondary to acute cardiac tamponade, as the pulmonary artery dissects into the pericardium; this diagnosis is often made postmortem. Nevertheless, with the proliferation of multidetector computed tomography (MDCT) as a diagnostic test, patients may be identified very early after symptom onset, prompting rapid intervention with decreased morbidity and mortality. We report a case of IPAH complicated by pulmonary artery aneurysm (PAA) and PAD, diagnosed by CT pulmonary angiogram (CTPA), and treated with bilateral lung transplantation, pulmonic valve replacement, and re-anastomosis of the donor main PA to a pulmonary valve conduit.
format article
author Luis Regalado, BS, MSc
Carol Vitellas, BA
Lindsay Wright, MD
Asvin Ganapathi, MD
Bryan A. Whitson, MD, PhD
Chiemezie Chianotu Amadi, MD, MA
author_facet Luis Regalado, BS, MSc
Carol Vitellas, BA
Lindsay Wright, MD
Asvin Ganapathi, MD
Bryan A. Whitson, MD, PhD
Chiemezie Chianotu Amadi, MD, MA
author_sort Luis Regalado, BS, MSc
title Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
title_short Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
title_full Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
title_fullStr Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
title_full_unstemmed Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
title_sort pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: a case report
publisher Elsevier
publishDate 2022
url https://doaj.org/article/979482b0c26b4674a9e890ffde928155
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