[72] Phaeochromocytoma of the bladder: Report of a case and review of the literature
Objective: To report on a case of phaeochromocytoma of the bladder and discuss general management principles of bladder phaeochromocytoma and the importance of long-term follow-up. Phaeochromocytomas are chromaffin cell tumours that are derived from neuroectodermal tissue of the adrenal gland and sy...
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| Autores principales: | , , , , , , , , , , , , |
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| Formato: | article |
| Lenguaje: | EN |
| Publicado: |
Taylor & Francis Group
2018
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| Materias: | |
| Acceso en línea: | https://doaj.org/article/a174493efe5e4a24b7bce56d47db1f53 |
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| Sumario: | Objective: To report on a case of phaeochromocytoma of the bladder and discuss general management principles of bladder phaeochromocytoma and the importance of long-term follow-up. Phaeochromocytomas are chromaffin cell tumours that are derived from neuroectodermal tissue of the adrenal gland and sympathetic paraganglia. These tumours can arise anywhere in the body from the skull (glomus and carotid bodies) to the bladder and prostatic glands. Phaeochromocytomas of the urinary bladder are rare tumours, accounting for ∼1% of extra-adrenal phaeochromocytomas and 0.06% of bladder tumours. Methods: A 13-year-old patient presented with paroxysmal symptoms consisting of headaches, palpitations, tinnitus and excessive sweating after each micturition and haematuria. Complementary investigations: ultrasonography, intravenous urography, and magnetic resonance imaging, suggested a circumscribed tumour with a 3-cm long axis in the bladder dome, and the diagnosis of bladder phaeochromocytoma was fixed after an endoscopic biopsy. Partial cystectomy was performed. Results: The postoperative course was uneventful, and the subsequent outcome was favourable with resolution of all symptoms with a follow-up of 10 years. Histological examination of the operative specimen confirmed the diagnosis of bladder phaeochromocytoma. Conclusion: Bladder phaeochromocytoma is a rare tumour. Treatment of this lesion requires the same preparation as for any other site of phaeochromocytoma. Partial cystectomy ensures radical and effective treatment. Long-term surveillance is necessary, as recurrences or metastases have been described 20 and 40 years after treatment. |
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