Management of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope

Hurler’s syndrome is a rare genetic disease characterized by progressive multiorgan accumulation of glycosaminoglycans. It is associated with progressive craniofacial, skeletal, and cardiac involvement, which increases the risk of anesthesia. Patients with Hurler’s syndrome could present as the wors...

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Autores principales: Keta D. Thakkar, Ajay P. Hrishi, Manikandan Sethuraman, Smita Vimala
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Lenguaje:EN
Publicado: Thieme Medical and Scientific Publishers Pvt. Ltd. 2020
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Acceso en línea:https://doaj.org/article/b71780bc834a4cee88c674b3fa258c06
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spelling oai:doaj.org-article:b71780bc834a4cee88c674b3fa258c062021-12-02T23:53:13ZManagement of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope2348-05482348-926X10.1055/s-0040-1714451https://doaj.org/article/b71780bc834a4cee88c674b3fa258c062020-08-01T00:00:00Zhttp://www.thieme-connect.de/DOI/DOI?10.1055/s-0040-1714451https://doaj.org/toc/2348-0548https://doaj.org/toc/2348-926XHurler’s syndrome is a rare genetic disease characterized by progressive multiorgan accumulation of glycosaminoglycans. It is associated with progressive craniofacial, skeletal, and cardiac involvement, which increases the risk of anesthesia. Patients with Hurler’s syndrome could present as the worst airway management problem an anesthesiologist could deal with due to abnormal upper airway anatomy and limited neck manipulation, owing to the atlantoaxial instability. We report a case of difficult airway scenario of a child with Hurler’s syndrome, leading to an apparent cannot ventilate cannot intubate scenario, which was managed successfully with the help of a C-MAC video laryngoscope with unique D-blade. In Hurler’s syndrome, C-MAC with D-blade is an excellent tool in establishing an airway in a pediatric difficult airway scenario. Moreover, D-blade C-MAC could be considered as the primary tool for establishing an airway in pediatric patients with Hurler’s syndrome.Keta D. ThakkarAjay P. HrishiManikandan SethuramanSmita VimalaThieme Medical and Scientific Publishers Pvt. Ltd.articlehurler’s syndromepediatric difficult airwayd-blade c-macAnesthesiologyRD78.3-87.3ENJournal of Neuroanaesthesiology and Critical Care, Vol 08, Iss 03, Pp 214-216 (2020)
institution DOAJ
collection DOAJ
language EN
topic hurler’s syndrome
pediatric difficult airway
d-blade c-mac
Anesthesiology
RD78.3-87.3
spellingShingle hurler’s syndrome
pediatric difficult airway
d-blade c-mac
Anesthesiology
RD78.3-87.3
Keta D. Thakkar
Ajay P. Hrishi
Manikandan Sethuraman
Smita Vimala
Management of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope
description Hurler’s syndrome is a rare genetic disease characterized by progressive multiorgan accumulation of glycosaminoglycans. It is associated with progressive craniofacial, skeletal, and cardiac involvement, which increases the risk of anesthesia. Patients with Hurler’s syndrome could present as the worst airway management problem an anesthesiologist could deal with due to abnormal upper airway anatomy and limited neck manipulation, owing to the atlantoaxial instability. We report a case of difficult airway scenario of a child with Hurler’s syndrome, leading to an apparent cannot ventilate cannot intubate scenario, which was managed successfully with the help of a C-MAC video laryngoscope with unique D-blade. In Hurler’s syndrome, C-MAC with D-blade is an excellent tool in establishing an airway in a pediatric difficult airway scenario. Moreover, D-blade C-MAC could be considered as the primary tool for establishing an airway in pediatric patients with Hurler’s syndrome.
format article
author Keta D. Thakkar
Ajay P. Hrishi
Manikandan Sethuraman
Smita Vimala
author_facet Keta D. Thakkar
Ajay P. Hrishi
Manikandan Sethuraman
Smita Vimala
author_sort Keta D. Thakkar
title Management of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope
title_short Management of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope
title_full Management of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope
title_fullStr Management of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope
title_full_unstemmed Management of a Difficult Airway Scenario in a Case of Hurler’s Syndrome with a D-Blade Video Laryngoscope
title_sort management of a difficult airway scenario in a case of hurler’s syndrome with a d-blade video laryngoscope
publisher Thieme Medical and Scientific Publishers Pvt. Ltd.
publishDate 2020
url https://doaj.org/article/b71780bc834a4cee88c674b3fa258c06
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