Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
Abstract Erdheim‐Chester disease (ECD) is a rare non‐Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51‐year‐old woman with a history of weakness, bone pain, xanthelasma palpebrarum, a...
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Wiley
2021
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oai:doaj.org-article:be4e4e7226b849178673b102528f7d872021-12-02T07:55:56ZErdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema2050-090410.1002/ccr3.4898https://doaj.org/article/be4e4e7226b849178673b102528f7d872021-10-01T00:00:00Zhttps://doi.org/10.1002/ccr3.4898https://doaj.org/toc/2050-0904Abstract Erdheim‐Chester disease (ECD) is a rare non‐Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51‐year‐old woman with a history of weakness, bone pain, xanthelasma palpebrarum, and diabetes insipidus. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus, bone pain, and multiorgan involvements.Faezeh Sadat NajiMinoo Sadat HajmiriZahra MazariFaeze SalahshourVahid SoleimaniManouchehr NakhjavaniMahboobeh HemmatabadiWileyarticlediabetes insipidusErdheim‐Chester diseasenon‐langerhans‐cell histiocytosisMedicineRMedicine (General)R5-920ENClinical Case Reports, Vol 9, Iss 10, Pp n/a-n/a (2021) |
institution |
DOAJ |
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DOAJ |
language |
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topic |
diabetes insipidus Erdheim‐Chester disease non‐langerhans‐cell histiocytosis Medicine R Medicine (General) R5-920 |
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diabetes insipidus Erdheim‐Chester disease non‐langerhans‐cell histiocytosis Medicine R Medicine (General) R5-920 Faezeh Sadat Naji Minoo Sadat Hajmiri Zahra Mazari Faeze Salahshour Vahid Soleimani Manouchehr Nakhjavani Mahboobeh Hemmatabadi Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema |
description |
Abstract Erdheim‐Chester disease (ECD) is a rare non‐Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51‐year‐old woman with a history of weakness, bone pain, xanthelasma palpebrarum, and diabetes insipidus. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus, bone pain, and multiorgan involvements. |
format |
article |
author |
Faezeh Sadat Naji Minoo Sadat Hajmiri Zahra Mazari Faeze Salahshour Vahid Soleimani Manouchehr Nakhjavani Mahboobeh Hemmatabadi |
author_facet |
Faezeh Sadat Naji Minoo Sadat Hajmiri Zahra Mazari Faeze Salahshour Vahid Soleimani Manouchehr Nakhjavani Mahboobeh Hemmatabadi |
author_sort |
Faezeh Sadat Naji |
title |
Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema |
title_short |
Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema |
title_full |
Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema |
title_fullStr |
Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema |
title_full_unstemmed |
Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema |
title_sort |
erdheim‐chester disease with long‐standing diabetes insipidus and generalized edema |
publisher |
Wiley |
publishDate |
2021 |
url |
https://doaj.org/article/be4e4e7226b849178673b102528f7d87 |
work_keys_str_mv |
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1718399124889403392 |