Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema

Abstract Erdheim‐Chester disease (ECD) is a rare non‐Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51‐year‐old woman with a history of weakness, bone pain, xanthelasma palpebrarum, a...

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Autores principales: Faezeh Sadat Naji, Minoo Sadat Hajmiri, Zahra Mazari, Faeze Salahshour, Vahid Soleimani, Manouchehr Nakhjavani, Mahboobeh Hemmatabadi
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Publicado: Wiley 2021
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spelling oai:doaj.org-article:be4e4e7226b849178673b102528f7d872021-12-02T07:55:56ZErdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema2050-090410.1002/ccr3.4898https://doaj.org/article/be4e4e7226b849178673b102528f7d872021-10-01T00:00:00Zhttps://doi.org/10.1002/ccr3.4898https://doaj.org/toc/2050-0904Abstract Erdheim‐Chester disease (ECD) is a rare non‐Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51‐year‐old woman with a history of weakness, bone pain, xanthelasma palpebrarum, and diabetes insipidus. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus, bone pain, and multiorgan involvements.Faezeh Sadat NajiMinoo Sadat HajmiriZahra MazariFaeze SalahshourVahid SoleimaniManouchehr NakhjavaniMahboobeh HemmatabadiWileyarticlediabetes insipidusErdheim‐Chester diseasenon‐langerhans‐cell histiocytosisMedicineRMedicine (General)R5-920ENClinical Case Reports, Vol 9, Iss 10, Pp n/a-n/a (2021)
institution DOAJ
collection DOAJ
language EN
topic diabetes insipidus
Erdheim‐Chester disease
non‐langerhans‐cell histiocytosis
Medicine
R
Medicine (General)
R5-920
spellingShingle diabetes insipidus
Erdheim‐Chester disease
non‐langerhans‐cell histiocytosis
Medicine
R
Medicine (General)
R5-920
Faezeh Sadat Naji
Minoo Sadat Hajmiri
Zahra Mazari
Faeze Salahshour
Vahid Soleimani
Manouchehr Nakhjavani
Mahboobeh Hemmatabadi
Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
description Abstract Erdheim‐Chester disease (ECD) is a rare non‐Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51‐year‐old woman with a history of weakness, bone pain, xanthelasma palpebrarum, and diabetes insipidus. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus, bone pain, and multiorgan involvements.
format article
author Faezeh Sadat Naji
Minoo Sadat Hajmiri
Zahra Mazari
Faeze Salahshour
Vahid Soleimani
Manouchehr Nakhjavani
Mahboobeh Hemmatabadi
author_facet Faezeh Sadat Naji
Minoo Sadat Hajmiri
Zahra Mazari
Faeze Salahshour
Vahid Soleimani
Manouchehr Nakhjavani
Mahboobeh Hemmatabadi
author_sort Faezeh Sadat Naji
title Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
title_short Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
title_full Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
title_fullStr Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
title_full_unstemmed Erdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
title_sort erdheim‐chester disease with long‐standing diabetes insipidus and generalized edema
publisher Wiley
publishDate 2021
url https://doaj.org/article/be4e4e7226b849178673b102528f7d87
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