Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review

Introduction: Pyloric atresia is a rare cause of congenital gastric outlet obstruction. It is often associated with epidermolysis bullosa (EB). Rarity and experience with 11 cases are the reason for this publication. Aims and Objectives: The aim and objective of this study is to present our experien...

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Autores principales:	Gungi Raghavendra Prasad, J V Subba Rao, Firdous Fatima, Fariha Anjum
Formato:	article
Lenguaje:	EN
Publicado:	Wolters Kluwer Medknow Publications 2021
Materias:	epidermolysis bullosa polyhydramnios pyloric atresia Pediatrics RJ1-570 Surgery RD1-811
Acceso en línea:	https://doaj.org/article/c555429cd392434196f36bbabc7f2fd8
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spelling	oai:doaj.org-article:c555429cd392434196f36bbabc7f2fd82021-11-19T10:42:06ZCongenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review0971-92611998-389110.4103/jiaps.JIAPS_295_20https://doaj.org/article/c555429cd392434196f36bbabc7f2fd82021-01-01T00:00:00Zhttp://www.jiaps.com/article.asp?issn=0971-9261;year=2021;volume=26;issue=6;spage=416;epage=420;aulast=Prasadhttps://doaj.org/toc/0971-9261https://doaj.org/toc/1998-3891Introduction: Pyloric atresia is a rare cause of congenital gastric outlet obstruction. It is often associated with epidermolysis bullosa (EB). Rarity and experience with 11 cases are the reason for this publication. Aims and Objectives: The aim and objective of this study is to present our experience of 11 cases of congenital pyloric atresia and correlate with available literature. Materials and Methods: This was retrospective cohort of 11 cases correlative comparative study. Data of all the 11 cases from 1982 to 2019 were collected, reviewed, and analyzed. The parameters studied included age, gender, antenatal diagnosis, postnatal diagnosis, preoperative management, intraoperative findings, postoperative course outcome, associated anomalies, and any genetic studies if done. All these parameters were compared with published data. Results: There were 11 cases in the present series with six boys and five girls. Most of them presented at varying periods from birth to day 1 of life. Eight cases of type 1 pyloric atresia, two cases of type 2 pyloric atresia, and one case of type 3 pyloric atresia constituted the cohort. Five out of 11 cases were associated with EB. Two out of six cases with isolated pyloric atresia and four out of five cases with EB died. Discussion: Congenital pyloric atresia may be isolated or associated with EB. Three varieties of pyloric atresia were described. Association with EB increases the mortality. Conclusions: Review and analysis of 11 cases of pyloric atresia compared with published literature is being reported.Gungi Raghavendra PrasadJ V Subba RaoFirdous FatimaFariha AnjumWolters Kluwer Medknow Publicationsarticleepidermolysis bullosapolyhydramniospyloric atresiaPediatricsRJ1-570SurgeryRD1-811ENJournal of Indian Association of Pediatric Surgeons, Vol 26, Iss 6, Pp 416-420 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	epidermolysis bullosa polyhydramnios pyloric atresia Pediatrics RJ1-570 Surgery RD1-811
spellingShingle	epidermolysis bullosa polyhydramnios pyloric atresia Pediatrics RJ1-570 Surgery RD1-811 Gungi Raghavendra Prasad J V Subba Rao Firdous Fatima Fariha Anjum Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review
description	Introduction: Pyloric atresia is a rare cause of congenital gastric outlet obstruction. It is often associated with epidermolysis bullosa (EB). Rarity and experience with 11 cases are the reason for this publication. Aims and Objectives: The aim and objective of this study is to present our experience of 11 cases of congenital pyloric atresia and correlate with available literature. Materials and Methods: This was retrospective cohort of 11 cases correlative comparative study. Data of all the 11 cases from 1982 to 2019 were collected, reviewed, and analyzed. The parameters studied included age, gender, antenatal diagnosis, postnatal diagnosis, preoperative management, intraoperative findings, postoperative course outcome, associated anomalies, and any genetic studies if done. All these parameters were compared with published data. Results: There were 11 cases in the present series with six boys and five girls. Most of them presented at varying periods from birth to day 1 of life. Eight cases of type 1 pyloric atresia, two cases of type 2 pyloric atresia, and one case of type 3 pyloric atresia constituted the cohort. Five out of 11 cases were associated with EB. Two out of six cases with isolated pyloric atresia and four out of five cases with EB died. Discussion: Congenital pyloric atresia may be isolated or associated with EB. Three varieties of pyloric atresia were described. Association with EB increases the mortality. Conclusions: Review and analysis of 11 cases of pyloric atresia compared with published literature is being reported.
format	article
author	Gungi Raghavendra Prasad J V Subba Rao Firdous Fatima Fariha Anjum
author_facet	Gungi Raghavendra Prasad J V Subba Rao Firdous Fatima Fariha Anjum
author_sort	Gungi Raghavendra Prasad
title	Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review
title_short	Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review
title_full	Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review
title_fullStr	Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review
title_full_unstemmed	Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review
title_sort	congenital pyloric atresia: experience with a series of 11 cases and collective review
publisher	Wolters Kluwer Medknow Publications
publishDate	2021
url	https://doaj.org/article/c555429cd392434196f36bbabc7f2fd8
work_keys_str_mv	AT gungiraghavendraprasad congenitalpyloricatresiaexperiencewithaseriesof11casesandcollectivereview AT jvsubbarao congenitalpyloricatresiaexperiencewithaseriesof11casesandcollectivereview AT firdousfatima congenitalpyloricatresiaexperiencewithaseriesof11casesandcollectivereview AT farihaanjum congenitalpyloricatresiaexperiencewithaseriesof11casesandcollectivereview
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Congenital Pyloric Atresia: Experience with a Series of 11 Cases and Collective Review

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