Cervicothoracic lipoblastoma: three case reports and review of literature

Abstract Background Lipoblastoma is a rare benign mesenchymal tumor of embryonal fat affecting mainly children below 3 years of age. It presents usually as a painless rapidly growing soft lobular mass in the extremities, trunk, and less frequently in the head-neck region. Preoperative imaging is use...

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Autores principales:	Alaa Ghallab, Mohamed Elmahmoud, Majed Alhadad, Khalil Albatniji, Ameen Alsaggaf, A. Gawad Elhendy, Alam Alshafi, Abdulwahab S. Aljubab
Formato:	article
Lenguaje:	EN
Publicado:	SpringerOpen 2021
Materias:	Lipoblastoma Mediastinal Surgical excision Prognosis Pediatrics RJ1-570 Surgery RD1-811
Acceso en línea:	https://doaj.org/article/d00caff4898b409eba22ad9e67916ca4
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spelling	oai:doaj.org-article:d00caff4898b409eba22ad9e67916ca42021-11-08T10:56:29ZCervicothoracic lipoblastoma: three case reports and review of literature10.1186/s43159-021-00121-82090-5394https://doaj.org/article/d00caff4898b409eba22ad9e67916ca42021-11-01T00:00:00Zhttps://doi.org/10.1186/s43159-021-00121-8https://doaj.org/toc/2090-5394Abstract Background Lipoblastoma is a rare benign mesenchymal tumor of embryonal fat affecting mainly children below 3 years of age. It presents usually as a painless rapidly growing soft lobular mass in the extremities, trunk, and less frequently in the head-neck region. Preoperative imaging is used to assess the extent of disease and aid surgical planning. Complete surgical excision without injury to surrounding vital structures is the treatment of choice. Case presentation We report three interesting lipoblastoma cases: mediastinal lipoblastoma with airway compression and ipsilateral diaphragmatic eventration, neck lipoblastoma with intrathoracic extension, and huge thoracic inlet lipoblastoma with compression of common carotid and Lt subclavian arteries, brachial plexus, and ipsilateral diaphragmatic eventration. Complete excision of lipoblastoma mass was done via neck incision in two cases, and the third case required thoracoscopic excision of intrathoracic remnant 6 months later. All three patients had an excellent outcome. Conclusions Management of cervicothoracic lipoblastoma is a surgical challenge due to the potential for rapid growth and extension to different fascial planes; however, successful excision can be achieved via a neck approach. Complete surgical excision is essential to prevent local recurrence and improve the outcome.Alaa GhallabMohamed ElmahmoudMajed AlhadadKhalil AlbatnijiAmeen AlsaggafA. Gawad ElhendyAlam AlshafiAbdulwahab S. AljubabSpringerOpenarticleLipoblastomaMediastinalSurgical excisionPrognosisPediatricsRJ1-570SurgeryRD1-811ENAnnals of Pediatric Surgery, Vol 17, Iss 1, Pp 1-7 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	Lipoblastoma Mediastinal Surgical excision Prognosis Pediatrics RJ1-570 Surgery RD1-811
spellingShingle	Lipoblastoma Mediastinal Surgical excision Prognosis Pediatrics RJ1-570 Surgery RD1-811 Alaa Ghallab Mohamed Elmahmoud Majed Alhadad Khalil Albatniji Ameen Alsaggaf A. Gawad Elhendy Alam Alshafi Abdulwahab S. Aljubab Cervicothoracic lipoblastoma: three case reports and review of literature
description	Abstract Background Lipoblastoma is a rare benign mesenchymal tumor of embryonal fat affecting mainly children below 3 years of age. It presents usually as a painless rapidly growing soft lobular mass in the extremities, trunk, and less frequently in the head-neck region. Preoperative imaging is used to assess the extent of disease and aid surgical planning. Complete surgical excision without injury to surrounding vital structures is the treatment of choice. Case presentation We report three interesting lipoblastoma cases: mediastinal lipoblastoma with airway compression and ipsilateral diaphragmatic eventration, neck lipoblastoma with intrathoracic extension, and huge thoracic inlet lipoblastoma with compression of common carotid and Lt subclavian arteries, brachial plexus, and ipsilateral diaphragmatic eventration. Complete excision of lipoblastoma mass was done via neck incision in two cases, and the third case required thoracoscopic excision of intrathoracic remnant 6 months later. All three patients had an excellent outcome. Conclusions Management of cervicothoracic lipoblastoma is a surgical challenge due to the potential for rapid growth and extension to different fascial planes; however, successful excision can be achieved via a neck approach. Complete surgical excision is essential to prevent local recurrence and improve the outcome.
format	article
author	Alaa Ghallab Mohamed Elmahmoud Majed Alhadad Khalil Albatniji Ameen Alsaggaf A. Gawad Elhendy Alam Alshafi Abdulwahab S. Aljubab
author_facet	Alaa Ghallab Mohamed Elmahmoud Majed Alhadad Khalil Albatniji Ameen Alsaggaf A. Gawad Elhendy Alam Alshafi Abdulwahab S. Aljubab
author_sort	Alaa Ghallab
title	Cervicothoracic lipoblastoma: three case reports and review of literature
title_short	Cervicothoracic lipoblastoma: three case reports and review of literature
title_full	Cervicothoracic lipoblastoma: three case reports and review of literature
title_fullStr	Cervicothoracic lipoblastoma: three case reports and review of literature
title_full_unstemmed	Cervicothoracic lipoblastoma: three case reports and review of literature
title_sort	cervicothoracic lipoblastoma: three case reports and review of literature
publisher	SpringerOpen
publishDate	2021
url	https://doaj.org/article/d00caff4898b409eba22ad9e67916ca4
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Cervicothoracic lipoblastoma: three case reports and review of literature

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