Long-term results of sirolimus treatment in lymphangioleiomyomatosis: a single referral centre experience

Abstract There are few published data on long-term treatment with sirolimus in lymphangioleiomyomatosis (LAM). The objective of this study was to describe the long-term effect of sirolimus in a series of LAM patients followed up in a referral centre, focusing on pulmonary function. We retrospectivel...

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Autores principales: Eva Revilla-López, Cristina Berastegui, Alejandra Méndez, Berta Sáez-Giménez, Victoria Ruiz de Miguel, Manuel López-Meseguer, Victor Monforte, Carlos Bravo, Miguel Angel Pujana, Maria Antonia Ramon, Susana Gómez-Ollés, Antonio Roman, The Vall d’Hebron Multidisciplinary Cystic Lung Disease Group
Formato: article
Lenguaje:EN
Publicado: Nature Portfolio 2021
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Acceso en línea:https://doaj.org/article/d41b30c353e24ea39210f9e0a6644bc1
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