Isolated endobronchial juvenile xanthogranuloma: a case report

Juvenile xanthogranuloma (JXG) is a rare non-Langerhans cell tumour usually diagnosed during infancy. The lesion is typically located in the skin; however, extracutaneous lesions have been described. The symptoms vary depending on the location and size of the lesion. Presented here is a case of 13-...

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Autores principales: Patrycja Sosnowska, Patrycja Antosik, Anna Ostałowska, Piotr Nogal, Przemysław Mańkowski
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Lenguaje:EN
Publicado: Termedia Publishing House 2020
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Acceso en línea:https://doaj.org/article/db6f80d8b79944e2bfe2eb6cbc567a24
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spelling oai:doaj.org-article:db6f80d8b79944e2bfe2eb6cbc567a242021-12-02T17:18:54ZIsolated endobronchial juvenile xanthogranuloma: a case report1428-25261897-430910.5114/wo.2020.97636https://doaj.org/article/db6f80d8b79944e2bfe2eb6cbc567a242020-07-01T00:00:00Zhttps://www.termedia.pl/Isolated-endobronchial-juvenile-xanthogranuloma-a-case-report,3,41418,1,1.htmlhttps://doaj.org/toc/1428-2526https://doaj.org/toc/1897-4309Juvenile xanthogranuloma (JXG) is a rare non-Langerhans cell tumour usually diagnosed during infancy. The lesion is typically located in the skin; however, extracutaneous lesions have been described. The symptoms vary depending on the location and size of the lesion. Presented here is a case of 13-year-old girl with this type of tumour located within the bronchus. She reported chest discomfort, difficulty breathing, and cough. A month prior to admission she had suffered from a respiratory tract infection. Prolonged surgical treatment was required due to the tumour’s atypical location and recurrence of the tumour following initial resection. Isolated pulmonary JXG is an extremely rare finding, which requires accurate diagnosis and careful planning of therapeutic treatment. Severe pulmonary symptoms, inconclusive histopathological examination, malignancy risk, and large tumour size are indications for radical surgical resection of the tumour. Non-surgical treatment with chemotherapy is useful in cases of inoperable tumours.Patrycja SosnowskaPatrycja AntosikAnna OstałowskaPiotr NogalPrzemysław MańkowskiTermedia Publishing Housearticlechemotherapy children juvenile xanthogranuloma non-langerhans cell tumour surgeryMedicineRENContemporary Oncology, Vol 24, Iss 3, Pp 200-202 (2020)
institution DOAJ
collection DOAJ
language EN
topic chemotherapy
children
juvenile xanthogranuloma
non-langerhans cell tumour
surgery
Medicine
R
spellingShingle chemotherapy
children
juvenile xanthogranuloma
non-langerhans cell tumour
surgery
Medicine
R
Patrycja Sosnowska
Patrycja Antosik
Anna Ostałowska
Piotr Nogal
Przemysław Mańkowski
Isolated endobronchial juvenile xanthogranuloma: a case report
description Juvenile xanthogranuloma (JXG) is a rare non-Langerhans cell tumour usually diagnosed during infancy. The lesion is typically located in the skin; however, extracutaneous lesions have been described. The symptoms vary depending on the location and size of the lesion. Presented here is a case of 13-year-old girl with this type of tumour located within the bronchus. She reported chest discomfort, difficulty breathing, and cough. A month prior to admission she had suffered from a respiratory tract infection. Prolonged surgical treatment was required due to the tumour’s atypical location and recurrence of the tumour following initial resection. Isolated pulmonary JXG is an extremely rare finding, which requires accurate diagnosis and careful planning of therapeutic treatment. Severe pulmonary symptoms, inconclusive histopathological examination, malignancy risk, and large tumour size are indications for radical surgical resection of the tumour. Non-surgical treatment with chemotherapy is useful in cases of inoperable tumours.
format article
author Patrycja Sosnowska
Patrycja Antosik
Anna Ostałowska
Piotr Nogal
Przemysław Mańkowski
author_facet Patrycja Sosnowska
Patrycja Antosik
Anna Ostałowska
Piotr Nogal
Przemysław Mańkowski
author_sort Patrycja Sosnowska
title Isolated endobronchial juvenile xanthogranuloma: a case report
title_short Isolated endobronchial juvenile xanthogranuloma: a case report
title_full Isolated endobronchial juvenile xanthogranuloma: a case report
title_fullStr Isolated endobronchial juvenile xanthogranuloma: a case report
title_full_unstemmed Isolated endobronchial juvenile xanthogranuloma: a case report
title_sort isolated endobronchial juvenile xanthogranuloma: a case report
publisher Termedia Publishing House
publishDate 2020
url https://doaj.org/article/db6f80d8b79944e2bfe2eb6cbc567a24
work_keys_str_mv AT patrycjasosnowska isolatedendobronchialjuvenilexanthogranulomaacasereport
AT patrycjaantosik isolatedendobronchialjuvenilexanthogranulomaacasereport
AT annaostałowska isolatedendobronchialjuvenilexanthogranulomaacasereport
AT piotrnogal isolatedendobronchialjuvenilexanthogranulomaacasereport
AT przemysławmankowski isolatedendobronchialjuvenilexanthogranulomaacasereport
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