Cleft palate in Pierre Robin sequence

Pierre Robin’s sequence PRS is a congenital malformative sequence with a retrognathism, a glossoptosis and an upper respiratory obstruction with an associated cleft palate. This malformative association can be disabling for both the child and his parents, because of its aesthetic, functional, psycho...

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Autores principales:	Oubejja Houda, Menbahi Imane, Elhasnaoui Chadi, Qurouach Souha, Benomar Ismail, Fouad Ettayebi Fouad
Formato:	article
Lenguaje:	EN FR
Publicado:	EDP Sciences 2021
Materias:	cleft palate retrognathism glossoptosis dysmorphia pierre-robin sequence surgery Environmental sciences GE1-350
Acceso en línea:	https://doaj.org/article/dd49f53dc9344262815c5faf876b1c75
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id	oai:doaj.org-article:dd49f53dc9344262815c5faf876b1c75
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spelling	oai:doaj.org-article:dd49f53dc9344262815c5faf876b1c752021-12-02T17:11:26ZCleft palate in Pierre Robin sequence2267-124210.1051/e3sconf/202131902013https://doaj.org/article/dd49f53dc9344262815c5faf876b1c752021-01-01T00:00:00Zhttps://www.e3s-conferences.org/articles/e3sconf/pdf/2021/95/e3sconf_vigisan_02013.pdfhttps://doaj.org/toc/2267-1242Pierre Robin’s sequence PRS is a congenital malformative sequence with a retrognathism, a glossoptosis and an upper respiratory obstruction with an associated cleft palate. This malformative association can be disabling for both the child and his parents, because of its aesthetic, functional, psychological and social impacts. Patients and methods: We have investigated 14 patients with PRS presenting cleft palates, collected over a period of 5 years, from March 2014 to November 2019 in the pediatric surgical emergencies department (PSE) in Rabat Children’s Hospital (HER). Results: Nine of the 14 patients had a complete cleft palate. The average age of intervention was 23 months ranging from 13 months to 4 years. The study showed a slight female predominance (n = 8, 57%). Regarding the treatment, 3 patients were treated with the Bardach’s technique, 3 had the Von Langenbeck’s technique, 3 had the Push-back technique and one patient who suffered from a post-operative persisting velar division was treated by veloplasty 3rd generation. The hospital stay was around 24 hours and the post-operative follow-up was uncomplicated for all our patients. Conclusion: Although we had a relatively high success with our approach, the complexity and lack of consensus regarding the management of Pierre Robin’s sequence still requires the involvement of a multidisciplinary team. The main aim is to give the best aesthetical and functional results in order to reduce the suffering of the PRS children and families.Oubejja HoudaMenbahi ImaneElhasnaoui ChadiQurouach SouhaBenomar IsmailFouad Ettayebi FouadEDP Sciencesarticlecleft palateretrognathismglossoptosisdysmorphiapierre-robin sequencesurgeryEnvironmental sciencesGE1-350ENFRE3S Web of Conferences, Vol 319, p 02013 (2021)
institution	DOAJ
collection	DOAJ
language	EN FR
topic	cleft palate retrognathism glossoptosis dysmorphia pierre-robin sequence surgery Environmental sciences GE1-350
spellingShingle	cleft palate retrognathism glossoptosis dysmorphia pierre-robin sequence surgery Environmental sciences GE1-350 Oubejja Houda Menbahi Imane Elhasnaoui Chadi Qurouach Souha Benomar Ismail Fouad Ettayebi Fouad Cleft palate in Pierre Robin sequence
description	Pierre Robin’s sequence PRS is a congenital malformative sequence with a retrognathism, a glossoptosis and an upper respiratory obstruction with an associated cleft palate. This malformative association can be disabling for both the child and his parents, because of its aesthetic, functional, psychological and social impacts. Patients and methods: We have investigated 14 patients with PRS presenting cleft palates, collected over a period of 5 years, from March 2014 to November 2019 in the pediatric surgical emergencies department (PSE) in Rabat Children’s Hospital (HER). Results: Nine of the 14 patients had a complete cleft palate. The average age of intervention was 23 months ranging from 13 months to 4 years. The study showed a slight female predominance (n = 8, 57%). Regarding the treatment, 3 patients were treated with the Bardach’s technique, 3 had the Von Langenbeck’s technique, 3 had the Push-back technique and one patient who suffered from a post-operative persisting velar division was treated by veloplasty 3rd generation. The hospital stay was around 24 hours and the post-operative follow-up was uncomplicated for all our patients. Conclusion: Although we had a relatively high success with our approach, the complexity and lack of consensus regarding the management of Pierre Robin’s sequence still requires the involvement of a multidisciplinary team. The main aim is to give the best aesthetical and functional results in order to reduce the suffering of the PRS children and families.
format	article
author	Oubejja Houda Menbahi Imane Elhasnaoui Chadi Qurouach Souha Benomar Ismail Fouad Ettayebi Fouad
author_facet	Oubejja Houda Menbahi Imane Elhasnaoui Chadi Qurouach Souha Benomar Ismail Fouad Ettayebi Fouad
author_sort	Oubejja Houda
title	Cleft palate in Pierre Robin sequence
title_short	Cleft palate in Pierre Robin sequence
title_full	Cleft palate in Pierre Robin sequence
title_fullStr	Cleft palate in Pierre Robin sequence
title_full_unstemmed	Cleft palate in Pierre Robin sequence
title_sort	cleft palate in pierre robin sequence
publisher	EDP Sciences
publishDate	2021
url	https://doaj.org/article/dd49f53dc9344262815c5faf876b1c75
work_keys_str_mv	AT oubejjahouda cleftpalateinpierrerobinsequence AT menbahiimane cleftpalateinpierrerobinsequence AT elhasnaouichadi cleftpalateinpierrerobinsequence AT qurouachsouha cleftpalateinpierrerobinsequence AT benomarismail cleftpalateinpierrerobinsequence AT fouadettayebifouad cleftpalateinpierrerobinsequence
_version_	1718381527892492288

Cleft palate in Pierre Robin sequence

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