Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update

Introduction: Oral and dental (OD) disorders in children with Rubinstein-Taybi syndrome (RTS) are frequent but not well-known by dentists and pediatricians due to the syndrome being extremely rare. Objective: To describe the OD findings observed in a 5-year-old girl with RTS and to update the liter...

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Autores principales:	Alejandro Carlos de la Parte-Serna, Ricardo Ortega-Soria, Gonzalo Oliván-Gonzalvo
Formato:	article
Lenguaje:	EN
Publicado:	Emergency Department of Hospital San Pedro (Logroño, Spain) 2021
Materias:	rubinstein-taybi syndrome odontostomatology disorders pediatric dentistry disabled persons determination of healthcare needs special patients talon cusps Medicine (General) R5-920
Acceso en línea:	https://doaj.org/article/df089e5c3d8242bca7929d33da38b336
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spelling	oai:doaj.org-article:df089e5c3d8242bca7929d33da38b3362021-12-02T17:45:29ZRubinstein-Taybi syndrome: principal oral and dental disorders and literature update10.5281/zenodo.44837652695-5075https://doaj.org/article/df089e5c3d8242bca7929d33da38b3362021-01-01T00:00:00Zhttps://doi.org/10.5281/zenodo.4483765https://doaj.org/toc/2695-5075Introduction: Oral and dental (OD) disorders in children with Rubinstein-Taybi syndrome (RTS) are frequent but not well-known by dentists and pediatricians due to the syndrome being extremely rare. Objective: To describe the OD findings observed in a 5-year-old girl with RTS and to update the literature. Clinical case: The patient presented the following OD manifestations: prominent lower lip, narrow mouth opening, narrow and arched palate, history of angular cheilitis, micrognathia, poor lingual motility, plaque and tartar, bleeding from gingival areas due to poor dental prophylaxis, and malocclusion in the form of an anterior open bite. These OD manifestations are seen in more than 40-60% of patients with RTS. Conclusions: Professionals who treat children with RTS should become aware of the advisability of referring them to the pediatric dentist from 1 year of age and performing check-ups every 6 months. Dental management is often difficult so collaboration with anesthesiologists is recommended in order to carry out a safe and effective treatment.Alejandro Carlos de la Parte-SernaRicardo Ortega-SoriaGonzalo Oliván-Gonzalvo Emergency Department of Hospital San Pedro (Logroño, Spain)articlerubinstein-taybi syndromeodontostomatology disorderspediatric dentistrydisabled personsdetermination of healthcare needsspecial patientstalon cuspsMedicine (General)R5-920ENIberoamerican Journal of Medicine, Vol 3, Iss 2, Pp 169-172 (2021)
institution	DOAJ
collection	DOAJ
language	EN
topic	rubinstein-taybi syndrome odontostomatology disorders pediatric dentistry disabled persons determination of healthcare needs special patients talon cusps Medicine (General) R5-920
spellingShingle	rubinstein-taybi syndrome odontostomatology disorders pediatric dentistry disabled persons determination of healthcare needs special patients talon cusps Medicine (General) R5-920 Alejandro Carlos de la Parte-Serna Ricardo Ortega-Soria Gonzalo Oliván-Gonzalvo Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update
description	Introduction: Oral and dental (OD) disorders in children with Rubinstein-Taybi syndrome (RTS) are frequent but not well-known by dentists and pediatricians due to the syndrome being extremely rare. Objective: To describe the OD findings observed in a 5-year-old girl with RTS and to update the literature. Clinical case: The patient presented the following OD manifestations: prominent lower lip, narrow mouth opening, narrow and arched palate, history of angular cheilitis, micrognathia, poor lingual motility, plaque and tartar, bleeding from gingival areas due to poor dental prophylaxis, and malocclusion in the form of an anterior open bite. These OD manifestations are seen in more than 40-60% of patients with RTS. Conclusions: Professionals who treat children with RTS should become aware of the advisability of referring them to the pediatric dentist from 1 year of age and performing check-ups every 6 months. Dental management is often difficult so collaboration with anesthesiologists is recommended in order to carry out a safe and effective treatment.
format	article
author	Alejandro Carlos de la Parte-Serna Ricardo Ortega-Soria Gonzalo Oliván-Gonzalvo
author_facet	Alejandro Carlos de la Parte-Serna Ricardo Ortega-Soria Gonzalo Oliván-Gonzalvo
author_sort	Alejandro Carlos de la Parte-Serna
title	Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update
title_short	Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update
title_full	Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update
title_fullStr	Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update
title_full_unstemmed	Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update
title_sort	rubinstein-taybi syndrome: principal oral and dental disorders and literature update
publisher	Emergency Department of Hospital San Pedro (Logroño, Spain)
publishDate	2021
url	https://doaj.org/article/df089e5c3d8242bca7929d33da38b336
work_keys_str_mv	AT alejandrocarlosdelaparteserna rubinsteintaybisyndromeprincipaloralanddentaldisordersandliteratureupdate AT ricardoortegasoria rubinsteintaybisyndromeprincipaloralanddentaldisordersandliteratureupdate AT gonzaloolivangonzalvo rubinsteintaybisyndromeprincipaloralanddentaldisordersandliteratureupdate
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Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update

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