Wissler-Fanconi syndrome and related diagnoses: a case report

Mustafa Q Albustani,1 Robert F Howard2 1Section of Medicine/Pediatrics, The University of Oklahoma College of Medicine, Tulsa, OK, USA; 2Division of Rheumatology, Utica Park Clinic, Tulsa, OK, USA Introduction: Wissler–Fanconi syndrome is a rare rheumatic syndrome that was first described...

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Autores principales:	Albustani MQ, Howard RF
Formato:	article
Lenguaje:	EN
Publicado:	Dove Medical Press 2016
Materias:	Wissler Fanconi Syndrome Adult stills disease subsepsis hyperergica subsepsis allergica Diseases of the musculoskeletal system RC925-935
Acceso en línea:	https://doaj.org/article/f0f5556ab00f42d69c17fc2fde9e9046
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spelling	oai:doaj.org-article:f0f5556ab00f42d69c17fc2fde9e90462021-12-02T00:27:49ZWissler-Fanconi syndrome and related diagnoses: a case report1179-156Xhttps://doaj.org/article/f0f5556ab00f42d69c17fc2fde9e90462016-06-01T00:00:00Zhttps://www.dovepress.com/wissler-fanconi-syndrome-and-related-diagnoses-a-case-report-peer-reviewed-article-OARRRhttps://doaj.org/toc/1179-156XMustafa Q Albustani,1 Robert F Howard2 1Section of Medicine/Pediatrics, The University of Oklahoma College of Medicine, Tulsa, OK, USA; 2Division of Rheumatology, Utica Park Clinic, Tulsa, OK, USA Introduction: Wissler–Fanconi syndrome is a rare rheumatic syndrome that was first described during the 1940s in Europe. Since then, many papers have been written that cover all aspects of this syndrome, most of which are in French and German language, with only a very few in English (none of them recent). We report here a case that fulfils the criteria for Wissler–Fanconi syndrome. Under the more general descriptive umbrella of Wissler–Fanconi syndrome, our patient also fulfils the Modified Jones criteria, and the 2010 American College of Rheumatology/European League Against Rheumatism (ACR/EULAR) classification criteria for rheumatoid arthritis, and was interpreted by other internists and another rheumatologist as fulfilling the Yamaguchi criteria for adult onset Still’s disease. Case presentation: A middle-aged female presented to the emergency department with shortness of breath and chest pain associated with fever, polyarthritis, and had a chronic polymorphic rash on the back and lower extremities. Blood analysis showed highly elevated inflammatory markers and rheumatoid factor. After ruling out other possible deferential diagnoses and reviewing the medical literature, the patient was diagnosed with Wissler–Fanconi syndrome. A combination of nonsteroidal anti-inflammatory drugs and steroids achieved complete remission. Conclusion: This case report highlights the important differential diagnosis that may be included under the nomenclature of Wissler–Fanconi syndrome (subsepsis hyperergica). Features of Wissler–Fanconi syndrome can be found in a differential diagnosis that includes true sepsis, acute rheumatic fever, rheumatoid arthritis, and adult onset Still’s disease. Keywords: Wissler–Fanconi syndrome, adult Still’s disease, subsepsis hyperergica, subsepsis allergica Albustani MQHoward RFDove Medical PressarticleWissler Fanconi SyndromeAdult stills diseasesubsepsis hyperergicasubsepsis allergicaDiseases of the musculoskeletal systemRC925-935ENOpen Access Rheumatology: Research and Reviews, Vol 2016, Iss Issue 1, Pp 73-75 (2016)
institution	DOAJ
collection	DOAJ
language	EN
topic	Wissler Fanconi Syndrome Adult stills disease subsepsis hyperergica subsepsis allergica Diseases of the musculoskeletal system RC925-935
spellingShingle	Wissler Fanconi Syndrome Adult stills disease subsepsis hyperergica subsepsis allergica Diseases of the musculoskeletal system RC925-935 Albustani MQ Howard RF Wissler-Fanconi syndrome and related diagnoses: a case report
description	Mustafa Q Albustani,1 Robert F Howard2 1Section of Medicine/Pediatrics, The University of Oklahoma College of Medicine, Tulsa, OK, USA; 2Division of Rheumatology, Utica Park Clinic, Tulsa, OK, USA Introduction: Wissler–Fanconi syndrome is a rare rheumatic syndrome that was first described during the 1940s in Europe. Since then, many papers have been written that cover all aspects of this syndrome, most of which are in French and German language, with only a very few in English (none of them recent). We report here a case that fulfils the criteria for Wissler–Fanconi syndrome. Under the more general descriptive umbrella of Wissler–Fanconi syndrome, our patient also fulfils the Modified Jones criteria, and the 2010 American College of Rheumatology/European League Against Rheumatism (ACR/EULAR) classification criteria for rheumatoid arthritis, and was interpreted by other internists and another rheumatologist as fulfilling the Yamaguchi criteria for adult onset Still’s disease. Case presentation: A middle-aged female presented to the emergency department with shortness of breath and chest pain associated with fever, polyarthritis, and had a chronic polymorphic rash on the back and lower extremities. Blood analysis showed highly elevated inflammatory markers and rheumatoid factor. After ruling out other possible deferential diagnoses and reviewing the medical literature, the patient was diagnosed with Wissler–Fanconi syndrome. A combination of nonsteroidal anti-inflammatory drugs and steroids achieved complete remission. Conclusion: This case report highlights the important differential diagnosis that may be included under the nomenclature of Wissler–Fanconi syndrome (subsepsis hyperergica). Features of Wissler–Fanconi syndrome can be found in a differential diagnosis that includes true sepsis, acute rheumatic fever, rheumatoid arthritis, and adult onset Still’s disease. Keywords: Wissler–Fanconi syndrome, adult Still’s disease, subsepsis hyperergica, subsepsis allergica
format	article
author	Albustani MQ Howard RF
author_facet	Albustani MQ Howard RF
author_sort	Albustani MQ
title	Wissler-Fanconi syndrome and related diagnoses: a case report
title_short	Wissler-Fanconi syndrome and related diagnoses: a case report
title_full	Wissler-Fanconi syndrome and related diagnoses: a case report
title_fullStr	Wissler-Fanconi syndrome and related diagnoses: a case report
title_full_unstemmed	Wissler-Fanconi syndrome and related diagnoses: a case report
title_sort	wissler-fanconi syndrome and related diagnoses: a case report
publisher	Dove Medical Press
publishDate	2016
url	https://doaj.org/article/f0f5556ab00f42d69c17fc2fde9e9046
work_keys_str_mv	AT albustanimq wisslerfanconisyndromeandrelateddiagnosesacasereport AT howardrf wisslerfanconisyndromeandrelateddiagnosesacasereport
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Wissler-Fanconi syndrome and related diagnoses: a case report

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