Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns

Hereditary angioedema (HAE) is a genetically caused orphan disease with a high risk of developing life-threatening attacks, thus requiring availability for up-to-date information on this problem for the doctors of any specialties. A limited number of observations determine the value of the analysis...

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Autores principales:	E. N. Bobrikova, A. R. Denisova, T. S. Kotomina, S. A. Serdotetskova, D. S. Fomina
Formato:	article
Lenguaje:	RU
Publicado:	SPb RAACI 2020
Materias:	angioedema hereditary pregnancy breastfeeding newborns children Immunologic diseases. Allergy RC581-607
Acceso en línea:	https://doaj.org/article/f20019f670644bdcb0ca9fc2dd266123
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spelling	oai:doaj.org-article:f20019f670644bdcb0ca9fc2dd2661232021-11-18T08:03:49ZSignificance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns1563-06252313-741X10.15789/1563-0625-SOI-1930https://doaj.org/article/f20019f670644bdcb0ca9fc2dd2661232020-05-01T00:00:00Zhttps://www.mimmun.ru/mimmun/article/view/1930https://doaj.org/toc/1563-0625https://doaj.org/toc/2313-741XHereditary angioedema (HAE) is a genetically caused orphan disease with a high risk of developing life-threatening attacks, thus requiring availability for up-to-date information on this problem for the doctors of any specialties. A limited number of observations determine the value of the analysis for each clinical case. Many facets of clinical manifestations, a list of predisposing and triggering factors, as well as limitations of some diagnostic and therapeutic algorithms, require the development of individual management schemes under distinct clinical situations. In this paper, we present the unique clinical cases with certain limitations, describing unexpected onset of the disease in the course of pregnancy, management aspects during delivery and post-delivery periods in a women with a previously confirmed HAE diagnosis. Adapted diagnostic algorithms of postnatal diagnostic verification are presented for children with burdened genetic history. We express some assumptions about involvement of a multidisciplinary team of specialists, personalized approach to building a management plan with an “online” correction depending on observation stage of НАЕ patient.E. N. BobrikovaA. R. DenisovaT. S. KotominaS. A. SerdotetskovaD. S. FominaSPb RAACIarticleangioedemahereditarypregnancybreastfeedingnewbornschildrenImmunologic diseases. AllergyRC581-607RUMedicinskaâ Immunologiâ, Vol 22, Iss 3, Pp 577-584 (2020)
institution	DOAJ
collection	DOAJ
language	RU
topic	angioedema hereditary pregnancy breastfeeding newborns children Immunologic diseases. Allergy RC581-607
spellingShingle	angioedema hereditary pregnancy breastfeeding newborns children Immunologic diseases. Allergy RC581-607 E. N. Bobrikova A. R. Denisova T. S. Kotomina S. A. Serdotetskova D. S. Fomina Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
description	Hereditary angioedema (HAE) is a genetically caused orphan disease with a high risk of developing life-threatening attacks, thus requiring availability for up-to-date information on this problem for the doctors of any specialties. A limited number of observations determine the value of the analysis for each clinical case. Many facets of clinical manifestations, a list of predisposing and triggering factors, as well as limitations of some diagnostic and therapeutic algorithms, require the development of individual management schemes under distinct clinical situations. In this paper, we present the unique clinical cases with certain limitations, describing unexpected onset of the disease in the course of pregnancy, management aspects during delivery and post-delivery periods in a women with a previously confirmed HAE diagnosis. Adapted diagnostic algorithms of postnatal diagnostic verification are presented for children with burdened genetic history. We express some assumptions about involvement of a multidisciplinary team of specialists, personalized approach to building a management plan with an “online” correction depending on observation stage of НАЕ patient.
format	article
author	E. N. Bobrikova A. R. Denisova T. S. Kotomina S. A. Serdotetskova D. S. Fomina
author_facet	E. N. Bobrikova A. R. Denisova T. S. Kotomina S. A. Serdotetskova D. S. Fomina
author_sort	E. N. Bobrikova
title	Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
title_short	Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
title_full	Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
title_fullStr	Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
title_full_unstemmed	Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
title_sort	significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
publisher	SPb RAACI
publishDate	2020
url	https://doaj.org/article/f20019f670644bdcb0ca9fc2dd266123
work_keys_str_mv	AT enbobrikova significanceofindividualmanagementplanforthepatientswithhereditarylymphangioedemaduringpregnancyandlactationandinnewborns AT ardenisova significanceofindividualmanagementplanforthepatientswithhereditarylymphangioedemaduringpregnancyandlactationandinnewborns AT tskotomina significanceofindividualmanagementplanforthepatientswithhereditarylymphangioedemaduringpregnancyandlactationandinnewborns AT saserdotetskova significanceofindividualmanagementplanforthepatientswithhereditarylymphangioedemaduringpregnancyandlactationandinnewborns AT dsfomina significanceofindividualmanagementplanforthepatientswithhereditarylymphangioedemaduringpregnancyandlactationandinnewborns
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Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns

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