Mastocitosis sistémica:: Un caso clínico

We report a 38 years old female who, since her childhood, had a history of precisely limited, fixed maculo papular dark brown cutaneous lesions in the trunk and extremities. These lesions become erythematous or urticarial after rubbing, medication intake or scratching. She also had frequent episodes...

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Autores principales: Mardones P,Pedro, Moyano G,Carlos, Peña N,Karina, Quijada S.,César
Lenguaje:Spanish / Castilian
Publicado: Sociedad Médica de Santiago 1998
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Acceso en línea:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98871998000700010
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spelling oai:scielo:S0034-988719980007000101999-06-15Mastocitosis sistémica:: Un caso clínicoMardones P,PedroMoyano G,CarlosPeña N,KarinaQuijada S.,César Mastocytosis/difuse cutaneous Urticaria pigmentosa H2 blockers We report a 38 years old female who, since her childhood, had a history of precisely limited, fixed maculo papular dark brown cutaneous lesions in the trunk and extremities. These lesions become erythematous or urticarial after rubbing, medication intake or scratching. She also had frequent episodes of tachycardia, flushing, headache, abdominal pain, arthralgia, diarrhea and vomiting. She was hospitalized in three occasions due to high frequency tachycardia, hypotension, generalized urticarial erythema and clouding of consciousness. Three of these episodes occurred after the ingestion of antinflammatory drugs or acetylsalicylic acid. Mastocyte infiltration was confirmed in skin and bone marrow biopsies and in bone scintiscan. The use of H1, H2 blockers and mastocyte stabilizers gave partial relief to the patient.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.126 n.7 19981998-07-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98871998000700010es10.4067/S0034-98871998000700010
institution Scielo Chile
collection Scielo Chile
language Spanish / Castilian
topic Mastocytosis/difuse cutaneous
Urticaria pigmentosa
H2 blockers
spellingShingle Mastocytosis/difuse cutaneous
Urticaria pigmentosa
H2 blockers
Mardones P,Pedro
Moyano G,Carlos
Peña N,Karina
Quijada S.,César
Mastocitosis sistémica:: Un caso clínico
description We report a 38 years old female who, since her childhood, had a history of precisely limited, fixed maculo papular dark brown cutaneous lesions in the trunk and extremities. These lesions become erythematous or urticarial after rubbing, medication intake or scratching. She also had frequent episodes of tachycardia, flushing, headache, abdominal pain, arthralgia, diarrhea and vomiting. She was hospitalized in three occasions due to high frequency tachycardia, hypotension, generalized urticarial erythema and clouding of consciousness. Three of these episodes occurred after the ingestion of antinflammatory drugs or acetylsalicylic acid. Mastocyte infiltration was confirmed in skin and bone marrow biopsies and in bone scintiscan. The use of H1, H2 blockers and mastocyte stabilizers gave partial relief to the patient.
author Mardones P,Pedro
Moyano G,Carlos
Peña N,Karina
Quijada S.,César
author_facet Mardones P,Pedro
Moyano G,Carlos
Peña N,Karina
Quijada S.,César
author_sort Mardones P,Pedro
title Mastocitosis sistémica:: Un caso clínico
title_short Mastocitosis sistémica:: Un caso clínico
title_full Mastocitosis sistémica:: Un caso clínico
title_fullStr Mastocitosis sistémica:: Un caso clínico
title_full_unstemmed Mastocitosis sistémica:: Un caso clínico
title_sort mastocitosis sistémica:: un caso clínico
publisher Sociedad Médica de Santiago
publishDate 1998
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98871998000700010
work_keys_str_mv AT mardonesppedro mastocitosissistemicauncasoclinico
AT moyanogcarlos mastocitosissistemicauncasoclinico
AT penankarina mastocitosissistemicauncasoclinico
AT quijadascesar mastocitosissistemicauncasoclinico
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