Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos

Although fibrosis and vasculopathy coexist in most patients with progressive systemic sclerosis, it is not clear if these events are the result of an unique etiologic factor or if one is consequence of the other. We report two cases of progressive systemic sclerosis that evolved to a renal scleroder...

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Autores principales:	Cuchacovich T,Miguel, Holuigue R,Gloria, Gatica R,Héctor, Alvo A,Miriam, Murray T,Guillermo
Lenguaje:	Spanish / Castilian
Publicado:	Sociedad Médica de Santiago 2000
Materias:	Cyclosporin Kidney failure, acute Penicillamine Scleroderma, systemic
Acceso en línea:	http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872000000100012
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id	oai:scielo:S0034-98872000000100012
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spelling	oai:scielo:S0034-988720000001000122000-05-25Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casosCuchacovich T,MiguelHoluigue R,GloriaGatica R,HéctorAlvo A,MiriamMurray T,Guillermo Cyclosporin Kidney failure, acute Penicillamine Scleroderma, systemic Although fibrosis and vasculopathy coexist in most patients with progressive systemic sclerosis, it is not clear if these events are the result of an unique etiologic factor or if one is consequence of the other. We report two cases of progressive systemic sclerosis that evolved to a renal scleroderma crisis. A 36 years old female presented with a Sjögren syndrome and painful subcutaneous nodules whose biopsy showed perivascular lymphocytic infiltration, perivascular thickening and normal skin. The ESR was 100 mm/h. She developed an hypertensive crisis and progressive renal failure, followed by a rapidly evolving progressive systemic sclerosis. The patient died in the course of this crisis. A 32 years old female with a progressive systemic sclerosis refractory to D-penicillamine treatment, receiving cyclosporin, presented a renal scleroderma crisis, that was successfully treated, with complete recovery of renal function. We highlight the different evolution of these cases, probably due to an early diagnosis and a better experience in the management of this condition. (Rev Méd Chile 2000; 128: 86-92)info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.128 n.1 20002000-01-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872000000100012es10.4067/S0034-98872000000100012
institution	Scielo Chile
collection	Scielo Chile
language	Spanish / Castilian
topic	Cyclosporin Kidney failure, acute Penicillamine Scleroderma, systemic
spellingShingle	Cyclosporin Kidney failure, acute Penicillamine Scleroderma, systemic Cuchacovich T,Miguel Holuigue R,Gloria Gatica R,Héctor Alvo A,Miriam Murray T,Guillermo Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos
description	Although fibrosis and vasculopathy coexist in most patients with progressive systemic sclerosis, it is not clear if these events are the result of an unique etiologic factor or if one is consequence of the other. We report two cases of progressive systemic sclerosis that evolved to a renal scleroderma crisis. A 36 years old female presented with a Sjögren syndrome and painful subcutaneous nodules whose biopsy showed perivascular lymphocytic infiltration, perivascular thickening and normal skin. The ESR was 100 mm/h. She developed an hypertensive crisis and progressive renal failure, followed by a rapidly evolving progressive systemic sclerosis. The patient died in the course of this crisis. A 32 years old female with a progressive systemic sclerosis refractory to D-penicillamine treatment, receiving cyclosporin, presented a renal scleroderma crisis, that was successfully treated, with complete recovery of renal function. We highlight the different evolution of these cases, probably due to an early diagnosis and a better experience in the management of this condition. (Rev Méd Chile 2000; 128: 86-92)
author	Cuchacovich T,Miguel Holuigue R,Gloria Gatica R,Héctor Alvo A,Miriam Murray T,Guillermo
author_facet	Cuchacovich T,Miguel Holuigue R,Gloria Gatica R,Héctor Alvo A,Miriam Murray T,Guillermo
author_sort	Cuchacovich T,Miguel
title	Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos
title_short	Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos
title_full	Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos
title_fullStr	Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos
title_full_unstemmed	Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos
title_sort	crisis de esclerodermia renal.: rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos
publisher	Sociedad Médica de Santiago
publishDate	2000
url	http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872000000100012
work_keys_str_mv	AT cuchacovichtmiguel crisisdeesclerodermiarenalroldelavasculopatiaesclerodermicaenlainducciondefibrosiscutaneovisceralendoscasos AT holuiguergloria crisisdeesclerodermiarenalroldelavasculopatiaesclerodermicaenlainducciondefibrosiscutaneovisceralendoscasos AT gaticarhector crisisdeesclerodermiarenalroldelavasculopatiaesclerodermicaenlainducciondefibrosiscutaneovisceralendoscasos AT alvoamiriam crisisdeesclerodermiarenalroldelavasculopatiaesclerodermicaenlainducciondefibrosiscutaneovisceralendoscasos AT murraytguillermo crisisdeesclerodermiarenalroldelavasculopatiaesclerodermicaenlainducciondefibrosiscutaneovisceralendoscasos
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Crisis de esclerodermia renal.: Rol de la vasculopatía esclerodérmica en la inducción de fibrosis cutáneo-visceral en dos casos

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