Falla auttonómica pura: Síndrome de Bradbury Eggleston

Pure Autonomic Failure is a progressive, adult onset, degenerative disorder of the autonomic nervous system characterized clinically by orthostatic hypotension, bladder, sexual and sudomotor dysfunction. Since there are no other associated somatic neurological deficits, this condition must be consid...

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Autores principales: Idiáquez C,Juan, Kaufmann,Horacio, Soza M,Marco, Necochea K,Cecilia
Lenguaje:Spanish / Castilian
Publicado: Sociedad Médica de Santiago 2005
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Acceso en línea:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872005000200010
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spelling oai:scielo:S0034-988720050002000102005-04-12Falla auttonómica pura: Síndrome de Bradbury EgglestonIdiáquez C,JuanKaufmann,HoracioSoza M,MarcoNecochea K,Cecilia Autonomic nervous system diseases Impotence Orthostatic hypotension, dysautonomic Pure Autonomic Failure is a progressive, adult onset, degenerative disorder of the autonomic nervous system characterized clinically by orthostatic hypotension, bladder, sexual and sudomotor dysfunction. Since there are no other associated somatic neurological deficits, this condition must be considered in the differential diagnosis of orthostatic hypotension. We report a 64 years old man with a history of seven years of autonomic dysfunction, with severe orthostatic hypotension, erectile and bladder dysfunction. Autonomic tests showed low circulating norepinephrine levels, sweating abnormalities with regional anhydrosis of the left side of the trunk and abnormal cardiovagal response, indicating generalized autonomic failure. Peripheral somatic neuropathies with autonomic involvement were excluded by normal electrophysiologic tests and the patient was diagnosed pure autonomic failure. Treatment with fludrocortisone and midodrine improved orthostatic tolerance (Rev Méd Chile 2005; 133: 215-8)info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.133 n.2 20052005-02-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872005000200010es10.4067/S0034-98872005000200010
institution Scielo Chile
collection Scielo Chile
language Spanish / Castilian
topic Autonomic nervous system diseases
Impotence
Orthostatic hypotension, dysautonomic
spellingShingle Autonomic nervous system diseases
Impotence
Orthostatic hypotension, dysautonomic
Idiáquez C,Juan
Kaufmann,Horacio
Soza M,Marco
Necochea K,Cecilia
Falla auttonómica pura: Síndrome de Bradbury Eggleston
description Pure Autonomic Failure is a progressive, adult onset, degenerative disorder of the autonomic nervous system characterized clinically by orthostatic hypotension, bladder, sexual and sudomotor dysfunction. Since there are no other associated somatic neurological deficits, this condition must be considered in the differential diagnosis of orthostatic hypotension. We report a 64 years old man with a history of seven years of autonomic dysfunction, with severe orthostatic hypotension, erectile and bladder dysfunction. Autonomic tests showed low circulating norepinephrine levels, sweating abnormalities with regional anhydrosis of the left side of the trunk and abnormal cardiovagal response, indicating generalized autonomic failure. Peripheral somatic neuropathies with autonomic involvement were excluded by normal electrophysiologic tests and the patient was diagnosed pure autonomic failure. Treatment with fludrocortisone and midodrine improved orthostatic tolerance (Rev Méd Chile 2005; 133: 215-8)
author Idiáquez C,Juan
Kaufmann,Horacio
Soza M,Marco
Necochea K,Cecilia
author_facet Idiáquez C,Juan
Kaufmann,Horacio
Soza M,Marco
Necochea K,Cecilia
author_sort Idiáquez C,Juan
title Falla auttonómica pura: Síndrome de Bradbury Eggleston
title_short Falla auttonómica pura: Síndrome de Bradbury Eggleston
title_full Falla auttonómica pura: Síndrome de Bradbury Eggleston
title_fullStr Falla auttonómica pura: Síndrome de Bradbury Eggleston
title_full_unstemmed Falla auttonómica pura: Síndrome de Bradbury Eggleston
title_sort falla auttonómica pura: síndrome de bradbury eggleston
publisher Sociedad Médica de Santiago
publishDate 2005
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872005000200010
work_keys_str_mv AT idiaquezcjuan fallaauttonomicapurasindromedebradburyeggleston
AT kaufmannhoracio fallaauttonomicapurasindromedebradburyeggleston
AT sozammarco fallaauttonomicapurasindromedebradburyeggleston
AT necocheakcecilia fallaauttonomicapurasindromedebradburyeggleston
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