Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínico
Aortic dissection is a life-threatening disease that requires immediate surgical intervention. Marfan syndrome is a hereditary disease with an autosomal dominant transmission, which affects the connective tissue, with skeletal, cardiovascular and ocular involvement. It is one of the most prevalent c...
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Sociedad Médica de Santiago
2009
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oai:scielo:S0034-988720090001000152009-04-13Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínicoEspinoza S,ChristianSelman A,RafaelPauchard T,FelipeRivera F,JuanIturra U,SebastiánMontecinos R,FernandoEliash D,HéctorUndurraga H,Francisco Aortic aneurysm Marfan syndrome Pregnancy complications cardiovascular Aortic dissection is a life-threatening disease that requires immediate surgical intervention. Marfan syndrome is a hereditary disease with an autosomal dominant transmission, which affects the connective tissue, with skeletal, cardiovascular and ocular involvement. It is one of the most prevalent connective tissue disorders, presenting a rísk of aortic dissection of approximately 1% even without dilatation of the aorta. When dissection occurs during pregnancy and requires surgical intervention (type A dissection), maternal mortality is high (2096-30%). We report a 38 year-old woman with Marfan syndrome that had an acute type A aortic dissection and severe aortic regurgitation at 37 weeks of gestation. The patient underwent a cesarean section and delivered a healthy baby. Afterwards, aortic valve repair and ascending aortic replacement was successfully performed under circulatory arrest with deep hypothermia. Additionally mitral valve repair for degenerative disease with posterior, autologous pericardium mitral valve ring was performed.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.137 n.1 20092009-01-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872009000100015es10.4067/S0034-98872009000100015 |
institution |
Scielo Chile |
collection |
Scielo Chile |
language |
Spanish / Castilian |
topic |
Aortic aneurysm Marfan syndrome Pregnancy complications cardiovascular |
spellingShingle |
Aortic aneurysm Marfan syndrome Pregnancy complications cardiovascular Espinoza S,Christian Selman A,Rafael Pauchard T,Felipe Rivera F,Juan Iturra U,Sebastián Montecinos R,Fernando Eliash D,Héctor Undurraga H,Francisco Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínico |
description |
Aortic dissection is a life-threatening disease that requires immediate surgical intervention. Marfan syndrome is a hereditary disease with an autosomal dominant transmission, which affects the connective tissue, with skeletal, cardiovascular and ocular involvement. It is one of the most prevalent connective tissue disorders, presenting a rísk of aortic dissection of approximately 1% even without dilatation of the aorta. When dissection occurs during pregnancy and requires surgical intervention (type A dissection), maternal mortality is high (2096-30%). We report a 38 year-old woman with Marfan syndrome that had an acute type A aortic dissection and severe aortic regurgitation at 37 weeks of gestation. The patient underwent a cesarean section and delivered a healthy baby. Afterwards, aortic valve repair and ascending aortic replacement was successfully performed under circulatory arrest with deep hypothermia. Additionally mitral valve repair for degenerative disease with posterior, autologous pericardium mitral valve ring was performed. |
author |
Espinoza S,Christian Selman A,Rafael Pauchard T,Felipe Rivera F,Juan Iturra U,Sebastián Montecinos R,Fernando Eliash D,Héctor Undurraga H,Francisco |
author_facet |
Espinoza S,Christian Selman A,Rafael Pauchard T,Felipe Rivera F,Juan Iturra U,Sebastián Montecinos R,Fernando Eliash D,Héctor Undurraga H,Francisco |
author_sort |
Espinoza S,Christian |
title |
Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínico |
title_short |
Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínico |
title_full |
Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínico |
title_fullStr |
Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínico |
title_full_unstemmed |
Disección aórtica y síndrome de Marfán en el embarazo: A propósito de un caso clínico |
title_sort |
disección aórtica y síndrome de marfán en el embarazo: a propósito de un caso clínico |
publisher |
Sociedad Médica de Santiago |
publishDate |
2009 |
url |
http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872009000100015 |
work_keys_str_mv |
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