Microlitiasis alveolar pulmonar: caso clínico

Pulmonary alveolar microlithiasis is an extremely rare disease characterized by intra-alveolar accumulation of calcified spherical particles (called microliths), due to a mutation of the gene encoding a membrane transport protein of the alveolar surface. Most patients are asymptomatic at diagnosis....

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Autores principales:	Fernández F,Cristina, Salinas F,Mauricio, de Grazia K,José Andrés, Díaz P,Juan Carlos
Lenguaje:	Spanish / Castilian
Publicado:	Sociedad Médica de Santiago 2014
Materias:	Lung diseases Pulmonary alveolar microlithiasis Tomography scanners X-Ray computed
Acceso en línea:	http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872014000500016
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spelling	oai:scielo:S0034-988720140005000162014-10-10Microlitiasis alveolar pulmonar: caso clínicoFernández F,CristinaSalinas F,Mauriciode Grazia K,José AndrésDíaz P,Juan Carlos Lung diseases Pulmonary alveolar microlithiasis Tomography scanners X-Ray computed Pulmonary alveolar microlithiasis is an extremely rare disease characterized by intra-alveolar accumulation of calcified spherical particles (called microliths), due to a mutation of the gene encoding a membrane transport protein of the alveolar surface. Most patients are asymptomatic at diagnosis. The course of the disease is slowly progressive, with development of pulmonary fibrosis and respiratory failure. The "sandstorm" pattern is the characteristic finding of this disease. We report a 39-year-old female presenting with progressive dyspnea. A chest X ray showed ground-glass opacities and a high resolution CT scan showed numerous calcified lung micronodules. A surgical lung biopsy confirmed the diagnosis of pulmonary alveolar microlithiasis.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.142 n.5 20142014-05-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872014000500016es10.4067/S0034-98872014000500016
institution	Scielo Chile
collection	Scielo Chile
language	Spanish / Castilian
topic	Lung diseases Pulmonary alveolar microlithiasis Tomography scanners X-Ray computed
spellingShingle	Lung diseases Pulmonary alveolar microlithiasis Tomography scanners X-Ray computed Fernández F,Cristina Salinas F,Mauricio de Grazia K,José Andrés Díaz P,Juan Carlos Microlitiasis alveolar pulmonar: caso clínico
description	Pulmonary alveolar microlithiasis is an extremely rare disease characterized by intra-alveolar accumulation of calcified spherical particles (called microliths), due to a mutation of the gene encoding a membrane transport protein of the alveolar surface. Most patients are asymptomatic at diagnosis. The course of the disease is slowly progressive, with development of pulmonary fibrosis and respiratory failure. The "sandstorm" pattern is the characteristic finding of this disease. We report a 39-year-old female presenting with progressive dyspnea. A chest X ray showed ground-glass opacities and a high resolution CT scan showed numerous calcified lung micronodules. A surgical lung biopsy confirmed the diagnosis of pulmonary alveolar microlithiasis.
author	Fernández F,Cristina Salinas F,Mauricio de Grazia K,José Andrés Díaz P,Juan Carlos
author_facet	Fernández F,Cristina Salinas F,Mauricio de Grazia K,José Andrés Díaz P,Juan Carlos
author_sort	Fernández F,Cristina
title	Microlitiasis alveolar pulmonar: caso clínico
title_short	Microlitiasis alveolar pulmonar: caso clínico
title_full	Microlitiasis alveolar pulmonar: caso clínico
title_fullStr	Microlitiasis alveolar pulmonar: caso clínico
title_full_unstemmed	Microlitiasis alveolar pulmonar: caso clínico
title_sort	microlitiasis alveolar pulmonar: caso clínico
publisher	Sociedad Médica de Santiago
publishDate	2014
url	http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872014000500016
work_keys_str_mv	AT fernandezfcristina microlitiasisalveolarpulmonarcasoclinico AT salinasfmauricio microlitiasisalveolarpulmonarcasoclinico AT degraziakjoseandres microlitiasisalveolarpulmonarcasoclinico AT diazpjuancarlos microlitiasisalveolarpulmonarcasoclinico
_version_	1718436757169504256

Microlitiasis alveolar pulmonar: caso clínico

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