Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura
T cell Prolymphocytic Leukemia (T-PLL) is a rare and aggressive mature T cell Lymphocyte Leukemia. Twenty five percent of cases present as a small cell variant, and only 5% as a cerebriform variant. We report a 58 year-old man with rapidly progressive severe leukocytosis, skin lesions, lymphadenopat...
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Sociedad Médica de Santiago
2016
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oai:scielo:S0034-988720160001000162016-03-17Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literaturaPeña,CamilaValladares,XimenaSoto,CarolinaEncina,AndreaMarinov,NedaUndurraga,María SoledadCabrera,María Elena Immunophenotyping Leukemia Prolymphocytic T-Cell Leukocytosis T cell Prolymphocytic Leukemia (T-PLL) is a rare and aggressive mature T cell Lymphocyte Leukemia. Twenty five percent of cases present as a small cell variant, and only 5% as a cerebriform variant. We report a 58 year-old man with rapidly progressive severe leukocytosis, skin lesions, lymphadenopathy, hepatosplenomegaly and pleural effusion. The lymphocytes had a cerebriform type. The diagnosis of T-PLL variant was made by morphology and immunophenotype study of peripheral blood. Karyotype was found to be complex. He was refractory to chemotherapy and died two months later.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.144 n.1 20162016-01-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872016000100016es10.4067/S0034-98872016000100016 |
institution |
Scielo Chile |
collection |
Scielo Chile |
language |
Spanish / Castilian |
topic |
Immunophenotyping Leukemia Prolymphocytic T-Cell Leukocytosis |
spellingShingle |
Immunophenotyping Leukemia Prolymphocytic T-Cell Leukocytosis Peña,Camila Valladares,Ximena Soto,Carolina Encina,Andrea Marinov,Neda Undurraga,María Soledad Cabrera,María Elena Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura |
description |
T cell Prolymphocytic Leukemia (T-PLL) is a rare and aggressive mature T cell Lymphocyte Leukemia. Twenty five percent of cases present as a small cell variant, and only 5% as a cerebriform variant. We report a 58 year-old man with rapidly progressive severe leukocytosis, skin lesions, lymphadenopathy, hepatosplenomegaly and pleural effusion. The lymphocytes had a cerebriform type. The diagnosis of T-PLL variant was made by morphology and immunophenotype study of peripheral blood. Karyotype was found to be complex. He was refractory to chemotherapy and died two months later. |
author |
Peña,Camila Valladares,Ximena Soto,Carolina Encina,Andrea Marinov,Neda Undurraga,María Soledad Cabrera,María Elena |
author_facet |
Peña,Camila Valladares,Ximena Soto,Carolina Encina,Andrea Marinov,Neda Undurraga,María Soledad Cabrera,María Elena |
author_sort |
Peña,Camila |
title |
Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura |
title_short |
Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura |
title_full |
Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura |
title_fullStr |
Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura |
title_full_unstemmed |
Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura |
title_sort |
leucemia prolinfocítica t variante de células cerebriformes: presentación de un caso y revisión de la literatura |
publisher |
Sociedad Médica de Santiago |
publishDate |
2016 |
url |
http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872016000100016 |
work_keys_str_mv |
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