Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura

T cell Prolymphocytic Leukemia (T-PLL) is a rare and aggressive mature T cell Lymphocyte Leukemia. Twenty five percent of cases present as a small cell variant, and only 5% as a cerebriform variant. We report a 58 year-old man with rapidly progressive severe leukocytosis, skin lesions, lymphadenopat...

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Autores principales: Peña,Camila, Valladares,Ximena, Soto,Carolina, Encina,Andrea, Marinov,Neda, Undurraga,María Soledad, Cabrera,María Elena
Lenguaje:Spanish / Castilian
Publicado: Sociedad Médica de Santiago 2016
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Acceso en línea:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872016000100016
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spelling oai:scielo:S0034-988720160001000162016-03-17Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literaturaPeña,CamilaValladares,XimenaSoto,CarolinaEncina,AndreaMarinov,NedaUndurraga,María SoledadCabrera,María Elena Immunophenotyping Leukemia Prolymphocytic T-Cell Leukocytosis T cell Prolymphocytic Leukemia (T-PLL) is a rare and aggressive mature T cell Lymphocyte Leukemia. Twenty five percent of cases present as a small cell variant, and only 5% as a cerebriform variant. We report a 58 year-old man with rapidly progressive severe leukocytosis, skin lesions, lymphadenopathy, hepatosplenomegaly and pleural effusion. The lymphocytes had a cerebriform type. The diagnosis of T-PLL variant was made by morphology and immunophenotype study of peripheral blood. Karyotype was found to be complex. He was refractory to chemotherapy and died two months later.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.144 n.1 20162016-01-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872016000100016es10.4067/S0034-98872016000100016
institution Scielo Chile
collection Scielo Chile
language Spanish / Castilian
topic Immunophenotyping
Leukemia Prolymphocytic T-Cell
Leukocytosis
spellingShingle Immunophenotyping
Leukemia Prolymphocytic T-Cell
Leukocytosis
Peña,Camila
Valladares,Ximena
Soto,Carolina
Encina,Andrea
Marinov,Neda
Undurraga,María Soledad
Cabrera,María Elena
Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura
description T cell Prolymphocytic Leukemia (T-PLL) is a rare and aggressive mature T cell Lymphocyte Leukemia. Twenty five percent of cases present as a small cell variant, and only 5% as a cerebriform variant. We report a 58 year-old man with rapidly progressive severe leukocytosis, skin lesions, lymphadenopathy, hepatosplenomegaly and pleural effusion. The lymphocytes had a cerebriform type. The diagnosis of T-PLL variant was made by morphology and immunophenotype study of peripheral blood. Karyotype was found to be complex. He was refractory to chemotherapy and died two months later.
author Peña,Camila
Valladares,Ximena
Soto,Carolina
Encina,Andrea
Marinov,Neda
Undurraga,María Soledad
Cabrera,María Elena
author_facet Peña,Camila
Valladares,Ximena
Soto,Carolina
Encina,Andrea
Marinov,Neda
Undurraga,María Soledad
Cabrera,María Elena
author_sort Peña,Camila
title Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura
title_short Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura
title_full Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura
title_fullStr Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura
title_full_unstemmed Leucemia prolinfocítica T variante de células cerebriformes: Presentación de un caso y revisión de la literatura
title_sort leucemia prolinfocítica t variante de células cerebriformes: presentación de un caso y revisión de la literatura
publisher Sociedad Médica de Santiago
publishDate 2016
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872016000100016
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