Síndrome de ALCAPA en adulto: Caso clínico

Anomalies of the origin of coronary arteries are detected in 0.5-1.5% of all angiographies. Anomalous origin of the left main trunk is the most uncommon and its origin from pulmonary artery in adults is exceptional, usually because it is associated with a short survival. We report a 49-year-old fema...

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Autores principales: Ugalde P,Héctor, Rozas A,Sebastián, Sanhueza F,María Ignacia, Yubini L,María Cecilia, García B,Sebastián
Lenguaje:Spanish / Castilian
Publicado: Sociedad Médica de Santiago 2017
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Acceso en línea:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000100016
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spelling oai:scielo:S0034-988720170001000162017-05-15Síndrome de ALCAPA en adulto: Caso clínicoUgalde P,HéctorRozas A,SebastiánSanhueza F,María IgnaciaYubini L,María CeciliaGarcía B,Sebastián Bland White Garland Syndrome Cardiovascular Abnormalities Coronary Vessel Anomalies Anomalies of the origin of coronary arteries are detected in 0.5-1.5% of all angiographies. Anomalous origin of the left main trunk is the most uncommon and its origin from pulmonary artery in adults is exceptional, usually because it is associated with a short survival. We report a 49-year-old female, presenting with a two months history of angina. The exercise electrocardiogram suggested ischemia. A coronary angiography was performed, showing the absence of the left main trunk in the left coronary sinus, a dilated right coronary artery, with no lesions and extensive collateral circulation to the anterior descending and circumflex arteries, with inverted flow and the left main trunk draining to the pulmonary artery. The left ventricle was mildly dilated with middle and apical anterior hypokinesia. Global systolic function was conserved. A surgical correction was decided, occluding the left main anomalous origin and performing a coronary artery bypass grafting from the left internal thoracic artery. The patient was discharged with no complications. At two years of follow-up she is symptom free and has a normal physical capacity.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.145 n.1 20172017-01-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000100016es10.4067/S0034-98872017000100016
institution Scielo Chile
collection Scielo Chile
language Spanish / Castilian
topic Bland White Garland Syndrome
Cardiovascular Abnormalities
Coronary Vessel Anomalies
spellingShingle Bland White Garland Syndrome
Cardiovascular Abnormalities
Coronary Vessel Anomalies
Ugalde P,Héctor
Rozas A,Sebastián
Sanhueza F,María Ignacia
Yubini L,María Cecilia
García B,Sebastián
Síndrome de ALCAPA en adulto: Caso clínico
description Anomalies of the origin of coronary arteries are detected in 0.5-1.5% of all angiographies. Anomalous origin of the left main trunk is the most uncommon and its origin from pulmonary artery in adults is exceptional, usually because it is associated with a short survival. We report a 49-year-old female, presenting with a two months history of angina. The exercise electrocardiogram suggested ischemia. A coronary angiography was performed, showing the absence of the left main trunk in the left coronary sinus, a dilated right coronary artery, with no lesions and extensive collateral circulation to the anterior descending and circumflex arteries, with inverted flow and the left main trunk draining to the pulmonary artery. The left ventricle was mildly dilated with middle and apical anterior hypokinesia. Global systolic function was conserved. A surgical correction was decided, occluding the left main anomalous origin and performing a coronary artery bypass grafting from the left internal thoracic artery. The patient was discharged with no complications. At two years of follow-up she is symptom free and has a normal physical capacity.
author Ugalde P,Héctor
Rozas A,Sebastián
Sanhueza F,María Ignacia
Yubini L,María Cecilia
García B,Sebastián
author_facet Ugalde P,Héctor
Rozas A,Sebastián
Sanhueza F,María Ignacia
Yubini L,María Cecilia
García B,Sebastián
author_sort Ugalde P,Héctor
title Síndrome de ALCAPA en adulto: Caso clínico
title_short Síndrome de ALCAPA en adulto: Caso clínico
title_full Síndrome de ALCAPA en adulto: Caso clínico
title_fullStr Síndrome de ALCAPA en adulto: Caso clínico
title_full_unstemmed Síndrome de ALCAPA en adulto: Caso clínico
title_sort síndrome de alcapa en adulto: caso clínico
publisher Sociedad Médica de Santiago
publishDate 2017
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000100016
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AT rozasasebastian sindromedealcapaenadultocasoclinico
AT sanhuezafmariaignacia sindromedealcapaenadultocasoclinico
AT yubinilmariacecilia sindromedealcapaenadultocasoclinico
AT garciabsebastian sindromedealcapaenadultocasoclinico
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