Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínico

Carney described a disorder characterized by the presence of several uncommon tumors which were pulmonary chondromas, gastric sarcomas and extra-adrenal paragangliomas. We report a 14 year-old girl in whom multiple gastric tumors were discovered during a study of an iron deficiency anemia and was su...

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Autores principales: Vega,Jorge, Navarro Subiabre,Jorge, Lovera Riquelme,Cristian, Opazo,Héctor, Santamarina,Mario
Lenguaje:Spanish / Castilian
Publicado: Sociedad Médica de Santiago 2017
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Acceso en línea:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000400014
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spelling oai:scielo:S0034-988720170004000142017-07-18Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínicoVega,JorgeNavarro Subiabre,JorgeLovera Riquelme,CristianOpazo,HéctorSantamarina,Mario Carney Complex Chondroma Leiomyosarcoma Paraganglioma Carney described a disorder characterized by the presence of several uncommon tumors which were pulmonary chondromas, gastric sarcomas and extra-adrenal paragangliomas. We report a 14 year-old girl in whom multiple gastric tumors were discovered during a study of an iron deficiency anemia and was subjected to a partial gastrectomy. At 25 years of age, she developed several pulmonary chondromas and at 33 years, a mediastinal tumor with features of an extra-adrenal paraganglioma was found. At 35 years of age, a total gastrectomy was performed to remove a gastrointestinal stromal tumor with excision of peritoneal and lymph node metastasis. One year later, the patient died due to liver failure secondary to liver metastases.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.145 n.4 20172017-04-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000400014es10.4067/S0034-98872017000400014
institution Scielo Chile
collection Scielo Chile
language Spanish / Castilian
topic Carney Complex
Chondroma
Leiomyosarcoma
Paraganglioma
spellingShingle Carney Complex
Chondroma
Leiomyosarcoma
Paraganglioma
Vega,Jorge
Navarro Subiabre,Jorge
Lovera Riquelme,Cristian
Opazo,Héctor
Santamarina,Mario
Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínico
description Carney described a disorder characterized by the presence of several uncommon tumors which were pulmonary chondromas, gastric sarcomas and extra-adrenal paragangliomas. We report a 14 year-old girl in whom multiple gastric tumors were discovered during a study of an iron deficiency anemia and was subjected to a partial gastrectomy. At 25 years of age, she developed several pulmonary chondromas and at 33 years, a mediastinal tumor with features of an extra-adrenal paraganglioma was found. At 35 years of age, a total gastrectomy was performed to remove a gastrointestinal stromal tumor with excision of peritoneal and lymph node metastasis. One year later, the patient died due to liver failure secondary to liver metastases.
author Vega,Jorge
Navarro Subiabre,Jorge
Lovera Riquelme,Cristian
Opazo,Héctor
Santamarina,Mario
author_facet Vega,Jorge
Navarro Subiabre,Jorge
Lovera Riquelme,Cristian
Opazo,Héctor
Santamarina,Mario
author_sort Vega,Jorge
title Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínico
title_short Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínico
title_full Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínico
title_fullStr Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínico
title_full_unstemmed Tríada de Carney. Una rara asociación de tumores infrecuentes: Caso clínico
title_sort tríada de carney. una rara asociación de tumores infrecuentes: caso clínico
publisher Sociedad Médica de Santiago
publishDate 2017
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000400014
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