Hemangioendotelioma epitelioide pulmonar: Reporte de un caso

Epithelioid hemangioendothelioma is a multifocal tumor that rarely metastasizes. It is difficult to diagnose, most often it is an incidental finding in young asymptomatic women. The radiologic pattern is heterogeneous. Histologic confirmation of Weibel-Palade bodies or immunohistochemistry based on...

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Autores principales: Quiroz,Manuel, Undurraga,Álvaro, Moya,Rafael, Fernández,Cristina, Bezares,Katiuska, Linacre,Virginia
Lenguaje:Spanish / Castilian
Publicado: Sociedad Médica de Santiago 2017
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Acceso en línea:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000500015
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spelling oai:scielo:S0034-988720170005000152017-11-16Hemangioendotelioma epitelioide pulmonar: Reporte de un casoQuiroz,ManuelUndurraga,ÁlvaroMoya,RafaelFernández,CristinaBezares,KatiuskaLinacre,Virginia Epitheliod Haemangioendothelioma Lung Neoplasms Weibel-Palade Bodies Epithelioid hemangioendothelioma is a multifocal tumor that rarely metastasizes. It is difficult to diagnose, most often it is an incidental finding in young asymptomatic women. The radiologic pattern is heterogeneous. Histologic confirmation of Weibel-Palade bodies or immunohistochemistry based on specific tumor markers such as factor VIII and CD34 are the most important finding to confirm the diagnosis. We report a 21 years old woman Presenting with cough and dyspnea. A chest X ray was suggestive of tuberculosis. Sputum smears were negative for acid fat bacilli and the tuberculin test was negative. A chest CAT scan showed multiple nodular lesions. A surgical biopsy of the lesions confirmed the presence of a hemangioendothelioma. The patient was initially treated with prednisone and azathioprine without response. Thereafter, the patient is without treatment and without evidence of disease progression.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.145 n.5 20172017-05-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000500015es10.4067/S0034-98872017000500015
institution Scielo Chile
collection Scielo Chile
language Spanish / Castilian
topic Epitheliod Haemangioendothelioma
Lung Neoplasms
Weibel-Palade Bodies
spellingShingle Epitheliod Haemangioendothelioma
Lung Neoplasms
Weibel-Palade Bodies
Quiroz,Manuel
Undurraga,Álvaro
Moya,Rafael
Fernández,Cristina
Bezares,Katiuska
Linacre,Virginia
Hemangioendotelioma epitelioide pulmonar: Reporte de un caso
description Epithelioid hemangioendothelioma is a multifocal tumor that rarely metastasizes. It is difficult to diagnose, most often it is an incidental finding in young asymptomatic women. The radiologic pattern is heterogeneous. Histologic confirmation of Weibel-Palade bodies or immunohistochemistry based on specific tumor markers such as factor VIII and CD34 are the most important finding to confirm the diagnosis. We report a 21 years old woman Presenting with cough and dyspnea. A chest X ray was suggestive of tuberculosis. Sputum smears were negative for acid fat bacilli and the tuberculin test was negative. A chest CAT scan showed multiple nodular lesions. A surgical biopsy of the lesions confirmed the presence of a hemangioendothelioma. The patient was initially treated with prednisone and azathioprine without response. Thereafter, the patient is without treatment and without evidence of disease progression.
author Quiroz,Manuel
Undurraga,Álvaro
Moya,Rafael
Fernández,Cristina
Bezares,Katiuska
Linacre,Virginia
author_facet Quiroz,Manuel
Undurraga,Álvaro
Moya,Rafael
Fernández,Cristina
Bezares,Katiuska
Linacre,Virginia
author_sort Quiroz,Manuel
title Hemangioendotelioma epitelioide pulmonar: Reporte de un caso
title_short Hemangioendotelioma epitelioide pulmonar: Reporte de un caso
title_full Hemangioendotelioma epitelioide pulmonar: Reporte de un caso
title_fullStr Hemangioendotelioma epitelioide pulmonar: Reporte de un caso
title_full_unstemmed Hemangioendotelioma epitelioide pulmonar: Reporte de un caso
title_sort hemangioendotelioma epitelioide pulmonar: reporte de un caso
publisher Sociedad Médica de Santiago
publishDate 2017
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872017000500015
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AT moyarafael hemangioendoteliomaepitelioidepulmonarreportedeuncaso
AT fernandezcristina hemangioendoteliomaepitelioidepulmonarreportedeuncaso
AT bezareskatiuska hemangioendoteliomaepitelioidepulmonarreportedeuncaso
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