Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión

Trichodysplasia spinulosa is a rare disease that occurs in the setting of immunosuppression, associated with tolerogenic therapy used in allograft recipients or patients with hematologic malignancies. Clinically, it is characterized by a centrofacial cutaneous eruption of erythematous papules with a...

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Autores principales:	Navarrete-Dechent,Cristián, Cevallos,Carolina, Manríquez,Juan Jorge, Salazar,Claudio, González,Sergio
Lenguaje:	Spanish / Castilian
Publicado:	Sociedad Médica de Santiago 2018
Materias:	Immunosuppression Pancytopenia Polyomavirus
Acceso en línea:	http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872018000100107
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spelling	oai:scielo:S0034-988720180001001072018-05-11Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresiónNavarrete-Dechent,CristiánCevallos,CarolinaManríquez,Juan JorgeSalazar,ClaudioGonzález,Sergio Immunosuppression Pancytopenia Polyomavirus Trichodysplasia spinulosa is a rare disease that occurs in the setting of immunosuppression, associated with tolerogenic therapy used in allograft recipients or patients with hematologic malignancies. Clinically, it is characterized by a centrofacial cutaneous eruption of erythematous papules with a central keratinous spicule, often associated with variable degrees of alopecia. Histologic findings are characteristic, and electron microscopy reveals the presence of trichodysplasia spinulosa associated polyomavirus. We report a 47-year-old woman with idiopathic autoimmune pancytopenia refractory to diverse immunosuppressant regimens, with clinical and pathologic findings compatible with the disease, in whom complementary studies were required to exclude other differential diagnoses.info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.146 n.1 20182018-01-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872018000100107es10.4067/s0034-98872018000100107
institution	Scielo Chile
collection	Scielo Chile
language	Spanish / Castilian
topic	Immunosuppression Pancytopenia Polyomavirus
spellingShingle	Immunosuppression Pancytopenia Polyomavirus Navarrete-Dechent,Cristián Cevallos,Carolina Manríquez,Juan Jorge Salazar,Claudio González,Sergio Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión
description	Trichodysplasia spinulosa is a rare disease that occurs in the setting of immunosuppression, associated with tolerogenic therapy used in allograft recipients or patients with hematologic malignancies. Clinically, it is characterized by a centrofacial cutaneous eruption of erythematous papules with a central keratinous spicule, often associated with variable degrees of alopecia. Histologic findings are characteristic, and electron microscopy reveals the presence of trichodysplasia spinulosa associated polyomavirus. We report a 47-year-old woman with idiopathic autoimmune pancytopenia refractory to diverse immunosuppressant regimens, with clinical and pathologic findings compatible with the disease, in whom complementary studies were required to exclude other differential diagnoses.
author	Navarrete-Dechent,Cristián Cevallos,Carolina Manríquez,Juan Jorge Salazar,Claudio González,Sergio
author_facet	Navarrete-Dechent,Cristián Cevallos,Carolina Manríquez,Juan Jorge Salazar,Claudio González,Sergio
author_sort	Navarrete-Dechent,Cristián
title	Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión
title_short	Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión
title_full	Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión
title_fullStr	Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión
title_full_unstemmed	Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión
title_sort	tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión
publisher	Sociedad Médica de Santiago
publishDate	2018
url	http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872018000100107
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Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión

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