Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric Patient
Cleidocranial Dysplasia (CCD) is an autosomal dominant bone disorder caused by a defect in the CBFA1 gene and characterized by skeletal, craniofacial and orodental anomalies. This paper describes the main aspects of a case of CCD from diagnosis and planning to the first step of the interventions. An...
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| Lenguaje: | English |
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Universidad de La Frontera. Facultad de Medicina
2016
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oai:scielo:S0718-381X20160002000212016-09-23Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric PatientMorikava,Francine SumieScariot,RafaelaMorosini,Imara de Almeida CastroSebastiani,AlineCosta,Delson JoãoFraiz,Fabian CalixtoFerreira,Fernanda Morais cleidocranial dysplasia bone diseases tooth supernumerary Cleidocranial Dysplasia (CCD) is an autosomal dominant bone disorder caused by a defect in the CBFA1 gene and characterized by skeletal, craniofacial and orodental anomalies. This paper describes the main aspects of a case of CCD from diagnosis and planning to the first step of the interventions. An 11-year-old male patient sought the pediatric dentistry clinic of the Federal University of Paraná (Brazil) with the complaint of the prolonged retention of nearly all his primary teeth. Clinical and imaging exams led to the diagnosis of CCD and the treatment plan was outlined. The first step consisted of the extraction of 4 primary, 2 permanent and 2 supernumerary teeth from the maxilla, followed by palate separation, traction of the impacted teeth and reverse traction of the maxilla. The patient remains in treatment. Clinical follow up as well as the awareness and motivation of the family are important factors in such cases.info:eu-repo/semantics/openAccessUniversidad de La Frontera. Facultad de MedicinaInternational journal of odontostomatology v.10 n.2 20162016-08-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0718-381X2016000200021en10.4067/S0718-381X2016000200021 |
| institution |
Scielo Chile |
| collection |
Scielo Chile |
| language |
English |
| topic |
cleidocranial dysplasia bone diseases tooth supernumerary |
| spellingShingle |
cleidocranial dysplasia bone diseases tooth supernumerary Morikava,Francine Sumie Scariot,Rafaela Morosini,Imara de Almeida Castro Sebastiani,Aline Costa,Delson João Fraiz,Fabian Calixto Ferreira,Fernanda Morais Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric Patient |
| description |
Cleidocranial Dysplasia (CCD) is an autosomal dominant bone disorder caused by a defect in the CBFA1 gene and characterized by skeletal, craniofacial and orodental anomalies. This paper describes the main aspects of a case of CCD from diagnosis and planning to the first step of the interventions. An 11-year-old male patient sought the pediatric dentistry clinic of the Federal University of Paraná (Brazil) with the complaint of the prolonged retention of nearly all his primary teeth. Clinical and imaging exams led to the diagnosis of CCD and the treatment plan was outlined. The first step consisted of the extraction of 4 primary, 2 permanent and 2 supernumerary teeth from the maxilla, followed by palate separation, traction of the impacted teeth and reverse traction of the maxilla. The patient remains in treatment. Clinical follow up as well as the awareness and motivation of the family are important factors in such cases. |
| author |
Morikava,Francine Sumie Scariot,Rafaela Morosini,Imara de Almeida Castro Sebastiani,Aline Costa,Delson João Fraiz,Fabian Calixto Ferreira,Fernanda Morais |
| author_facet |
Morikava,Francine Sumie Scariot,Rafaela Morosini,Imara de Almeida Castro Sebastiani,Aline Costa,Delson João Fraiz,Fabian Calixto Ferreira,Fernanda Morais |
| author_sort |
Morikava,Francine Sumie |
| title |
Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric Patient |
| title_short |
Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric Patient |
| title_full |
Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric Patient |
| title_fullStr |
Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric Patient |
| title_full_unstemmed |
Cleidocranial Dysplasia: Diagnosis, Surgical and Orthodontic Planning and Interventions in a Pediatric Patient |
| title_sort |
cleidocranial dysplasia: diagnosis, surgical and orthodontic planning and interventions in a pediatric patient |
| publisher |
Universidad de La Frontera. Facultad de Medicina |
| publishDate |
2016 |
| url |
http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0718-381X2016000200021 |
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