Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary Approach

ABSTRACT: Gorlin-Goltz Syndrome is a genetic disorder characterized by a series of clinical changes, including the presence of multiple odontogenic keratocysts and nevus basal cell carcinomas. As these lesions involve the maxillofacial region and can evolve to severe sequelae, it is essential that t...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Bachesk,Andressa Bolognesi, Peder,Silvia Natália Souza de, Lustosa,Romulo Maciel, Nogueira,Lucas Costa, Iwaki-Filho,Liogi
Lenguaje:English
Publicado: Universidad de La Frontera. Facultad de Medicina 2021
Materias:
Acceso en línea:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0718-381X2021000100189
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!
id oai:scielo:S0718-381X2021000100189
record_format dspace
spelling oai:scielo:S0718-381X20210001001892021-02-16Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary ApproachBachesk,Andressa BolognesiPeder,Silvia Natália Souza deLustosa,Romulo MacielNogueira,Lucas CostaIwaki-Filho,Liogi basal cell carcinoma clinical diagnosis combined modality therapy Gorlin-Goltz syndrome keratocystic odontogenic ABSTRACT: Gorlin-Goltz Syndrome is a genetic disorder characterized by a series of clinical changes, including the presence of multiple odontogenic keratocysts and nevus basal cell carcinomas. As these lesions involve the maxillofacial region and can evolve to severe sequelae, it is essential that the dental surgeon recognize this pathology, in order to promote a correct investigation and early multidisciplinary diagnosis and treatment. The treatment for the cysts varies according to the lesion’s characteristics and location, and therefore, the request for complementary exams is essential. According to literature, the approach varies from conservative to more invasive, and several supporting therapies are mentioned. Thus, this article aims to report a case of a young patient diagnosed with Gorlin-Goltz Syndrome by a dental surgeon, who treated conservatively and interdisciplinarly, and obtained a satisfactory result. In addition, it makes a bibliographic review on this genetic condition, elucidating its therapeutic forms.info:eu-repo/semantics/openAccessUniversidad de La Frontera. Facultad de MedicinaInternational journal of odontostomatology v.15 n.1 20212021-03-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0718-381X2021000100189en10.4067/S0718-381X2021000100189
institution Scielo Chile
collection Scielo Chile
language English
topic basal cell carcinoma
clinical diagnosis
combined modality therapy
Gorlin-Goltz syndrome
keratocystic odontogenic
spellingShingle basal cell carcinoma
clinical diagnosis
combined modality therapy
Gorlin-Goltz syndrome
keratocystic odontogenic
Bachesk,Andressa Bolognesi
Peder,Silvia Natália Souza de
Lustosa,Romulo Maciel
Nogueira,Lucas Costa
Iwaki-Filho,Liogi
Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary Approach
description ABSTRACT: Gorlin-Goltz Syndrome is a genetic disorder characterized by a series of clinical changes, including the presence of multiple odontogenic keratocysts and nevus basal cell carcinomas. As these lesions involve the maxillofacial region and can evolve to severe sequelae, it is essential that the dental surgeon recognize this pathology, in order to promote a correct investigation and early multidisciplinary diagnosis and treatment. The treatment for the cysts varies according to the lesion’s characteristics and location, and therefore, the request for complementary exams is essential. According to literature, the approach varies from conservative to more invasive, and several supporting therapies are mentioned. Thus, this article aims to report a case of a young patient diagnosed with Gorlin-Goltz Syndrome by a dental surgeon, who treated conservatively and interdisciplinarly, and obtained a satisfactory result. In addition, it makes a bibliographic review on this genetic condition, elucidating its therapeutic forms.
author Bachesk,Andressa Bolognesi
Peder,Silvia Natália Souza de
Lustosa,Romulo Maciel
Nogueira,Lucas Costa
Iwaki-Filho,Liogi
author_facet Bachesk,Andressa Bolognesi
Peder,Silvia Natália Souza de
Lustosa,Romulo Maciel
Nogueira,Lucas Costa
Iwaki-Filho,Liogi
author_sort Bachesk,Andressa Bolognesi
title Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary Approach
title_short Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary Approach
title_full Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary Approach
title_fullStr Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary Approach
title_full_unstemmed Gorlin-Goltz Syndrome: The importance of Clinical Investigation and a Multidisciplinary Approach
title_sort gorlin-goltz syndrome: the importance of clinical investigation and a multidisciplinary approach
publisher Universidad de La Frontera. Facultad de Medicina
publishDate 2021
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0718-381X2021000100189
work_keys_str_mv AT bacheskandressabolognesi gorlingoltzsyndrometheimportanceofclinicalinvestigationandamultidisciplinaryapproach
AT pedersilvianataliasouzade gorlingoltzsyndrometheimportanceofclinicalinvestigationandamultidisciplinaryapproach
AT lustosaromulomaciel gorlingoltzsyndrometheimportanceofclinicalinvestigationandamultidisciplinaryapproach
AT nogueiralucascosta gorlingoltzsyndrometheimportanceofclinicalinvestigationandamultidisciplinaryapproach
AT iwakifilholiogi gorlingoltzsyndrometheimportanceofclinicalinvestigationandamultidisciplinaryapproach
_version_ 1714204047682043904