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Huntington Disease
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41por Kaly A. Mueller, Kelly E. Glajch, Megan N. Huizenga, Remi A. Wilson, Eric J. Granucci, Amanda M. Dios, Adelaide R. Tousley, Maria Iuliano, Elizabeth Weisman, Michael J. LaQuaglia, Marian DiFiglia, Kimberly Kegel-Gleason, Khashayar Vakili, Ghazaleh Sadri-Vakili“... in Huntington’s disease (HD) pathogenesis. Our results demonstrate a significant increase in phosphorylated MST1...”
Publicado 2018
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42por Andreas Neueder, Christian Landles, Rhia Ghosh, David Howland, Richard H. Myers, Richard L. M. Faull, Sarah J. Tabrizi, Gillian P. Bates“... and is present in all knock-in mouse models of Huntington’s disease (HD) with CAG lengths of 50 and above...”
Publicado 2017
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43por Zheng Wu, Matthew Parry, Xiao-Yi Hou, Min-Hui Liu, Hui Wang, Rachel Cain, Zi-Fei Pei, Yu-Chen Chen, Zi-Yuan Guo, Sambangi Abhijeet, Gong Chen“... this procedure in the R6/2 mouse model of Huntington’s disease, targeting astrocytes in the striatum, converting...”
Publicado 2020
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44por Ravi Kiran Reddy Kalathur, José Pedro Pinto, Biswanath Sahoo, Gautam Chaurasia, Matthias E. Futschik“...Abstract Huntington’s disease (HD) is a progressive and fatal neurodegenerative disorder caused...”
Publicado 2017
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45por Travis Cruickshank, Tenielle Porter, Simon M. Laws, Mel Ziman, Danielle M. Bartlett“... hypothalamic–pituitary–adrenal (HPA) axis function in Huntington’s disease (HD). These differences are presumed...”
Publicado 2021
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46por Huajing You, Tengteng Wu, Gang Du, Gang Du, Yue Huang, Yue Huang, Yixuan Zeng, Lishan Lin, Dingbang Chen, Chao Wu, Xunhua Li, Jean-marc Burgunder, Zhong PeiMaterias: “...Huntington's disease...”
Publicado 2021
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48por Hongyu Zhang, Chunlei Zhang, Jean Vincent, Diana Zala, Caroline Benstaali, Matthieu Sainlos, Dolors Grillo-Bosch, Sophie Daburon, Françoise Coussen, Yoon Cho, Denis J. David, Frederic Saudou, Yann Humeau, Daniel Choquet“...Cognitive decline in Huntington’s disease (HD) may be due to impaired hippocampal synaptic...”
Publicado 2018
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49por Michael A. Mason, Casandra Gomez-Paredes, Kirupa Sathasivam, Andreas Neueder, Aikaterini-Smaragdi Papadopoulou, Gillian P. Bates“..., by manipulating SRSF6 levels in Huntington’s disease models in which an expanded CAG repeat had been knocked...”
Publicado 2020
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50por Mehdi Eshraghi, Pabalu P. Karunadharma, Juliana Blin, Neelam Shahani, Emiliano P. Ricci, Audrey Michel, Nicolai T. Urban, Nicole Galli, Manish Sharma, Uri Nimrod Ramírez-Jarquín, Katie Florescu, Jennifer Hernandez, Srinivasa Subramaniam“...Huntington disease (HD) is a neurodegenerative disorder caused by the expansion of a polyglutamine...”
Publicado 2021
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52por Mario Quarantelli, Elena Salvatore, Sara Maria Delle Acque Giorgio, Alessandro Filla, Amedeo Cervo, Cinzia Valeria Russo, Sirio Cocozza, Marco Massarelli, Arturo Brunetti, Giuseppe De Michele“...Previous MRI studies of functional connectivity in pre-symptomatic mutation carriers of Huntington...”
Publicado 2013
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53“...Huntington disease (HD) is an inherited neurodegenerative disease characterized by motor, cognitive...”
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54por Daniel Todd, Ian Gowers, Simon J Dowler, Michael D Wall, George McAllister, David F Fischer, Sipke Dijkstra, Silvina A Fratantoni, Rhea van de Bospoort, Jessica Veenman-Koepke, Geraldine Flynn, Jamshid Arjomand, Celia Dominguez, Ignacio Munoz-Sanjuan, John Wityak, Jonathan A Bard“...Huntington's disease (HD) is a devastating, genetic neurodegenerative disease caused by a tri...”
Publicado 2014
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55por Matthew P. Parsons, Matthieu P. Vanni, Cameron L. Woodard, Rujun Kang, Timothy H. Murphy, Lynn A. Raymond“...Huntington disease (HD) has been linked via biochemical uptake assays to impaired glutamate...”
Publicado 2016
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56por Tara L Walker, Geoff W Turnbull, Eirinn W Mackay, Anthony J Hannan, Perry F Bartlett“... in the subventricular zone (SVZ) and hippocampus of the R6/1 transgenic mouse model of Huntington's disease (HD). Our...”
Publicado 2011
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57por Albert Giralt, Veronica Brito, Quentin Chevy, Clémence Simonnet, Yo Otsu, Carmen Cifuentes-Díaz, Benoit de Pins, Renata Coura, Jordi Alberch, Sílvia Ginés, Jean-Christophe Poncer, Jean-Antoine Girault“... deficits in a mouse model of Huntington’s disease....”
Publicado 2017
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60por Dmitry A. Nedosekin, TsungYen Chen, Srinivas Ayyadevara, Vladimir P. Zharov, Robert J. Shmookler Reis“... disorders including Alzheimer’s, Parkinson’s and Huntington’s diseases. Little progress has been made...”
Publicado 2021
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