Plasma lipidomic analysis shows a disease progression signature in mdx mice
Abstract Duchenne muscular dystrophy (DMD) is a rare genetic disorder affecting paediatric patients. The disease course is characterized by loss of muscle mass, which is rapidly substituted by fibrotic and adipose tissue. Clinical and preclinical models have clarified the processes leading to muscle...
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Auteurs principaux: | Roula Tsonaka, Alexandre Seyer, Annemieke Aartsma-Rus, Pietro Spitali |
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Format: | article |
Langue: | EN |
Publié: |
Nature Portfolio
2021
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Accès en ligne: | https://doaj.org/article/bb7a18b1cea74e9bb5c40a2992c9ea8e |
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