Fibrodisplasia osificante progresiva plus por una variante patogénica del gen ACVR1: Caso clínico

Fibrodysplasia ossificans progressiva (FOP) or myositis ossificans, is a genetic disease, with a prevalence of 1 in 2.000.000. It is caused by pathogenic variants in ACVR1 gene and characterized by soft tissue heterotopic ossification, starting in the second decade of life. It is associated to early...

Description complète

Enregistré dans:
Détails bibliographiques
Auteurs principaux: Contreras-Olea,Oscar, Goecke-Hochberger,Carola, Rumié-Carmi,Hana Karime, Lobo-Avilés,Rosendo, Mellado-Sagredo,Cecilia, Avila-Smirnow,Daniela
Langue:Spanish / Castilian
Publié: Sociedad Médica de Santiago 2019
Sujets:
Accès en ligne:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872019000300384
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!